{"id":"W4245734851","doi":"10.1016/j.nmd.2020.08.200","title":"CONGENITAL MUSCULAR DYSTROPHIES","year":2020,"lang":"en","type":"article","venue":"Neuromuscular Disorders","topic":"Cellular transport and secretion","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"Concordia University","funders":"","keywords":"Muscular dystrophy; Pathology; Congenital muscular dystrophy; Dystroglycan; Biology; Neurodegeneration; Neuropathology; Muscle weakness; Atrophy; Purkinje cell; Spinal muscular atrophy; Neuroscience; Medicine; Cerebellum; Anatomy; Cell biology; Genetics; Disease; Laminin","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002034916,0.001083586,0.0004552202,0.001266277,0.0008575766,0.0004158458,0.0004535029,0.0009389848,0.01321979],"category_scores_gemma":[0.0006642137,0.0001978715,0.0002167833,0.000919662,0.001087211,0.0003471025,0.000885499,0.0005542741,0.001907276],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005516199,"about_ca_system_score_gemma":0.0003373289,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002189352,"about_ca_topic_score_gemma":0.002009755,"domain_scores_codex":[0.9997492,0.00003835821,0.00003038015,0.00006827157,0.00006171252,0.00005205698],"domain_scores_gemma":[0.9996858,0.0001084339,0.00008189098,0.00003189275,0.00003442448,0.00005756242],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"not_applicable","study_design_scores_codex":[0.001780355,0.00008634511,0.03925523,0.001207781,0.0002705981,0.3622108,0.001150357,0.001012342,0.4205032,0.03115302,0.02137706,0.1199929],"study_design_scores_gemma":[0.0001390635,0.0004759641,0.2030015,0.0002811916,0.0004502098,0.53954,0.0005203747,0.001549993,0.1109482,0.004658383,0.1383417,0.00009353975],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"review","genre_scores_codex":[0.8435823,0.02719994,0.005736504,0.002071149,0.0006005968,0.00008637272,0.005340957,0.001081381,0.1143007],"genre_scores_gemma":[0.9749056,0.003051505,0.001866581,0.0002564705,0.0001757727,0.00002492526,0.00107803,0.0001001131,0.01854118],"genre_candidate":"review","genre_consensus":null,"teacher_disagreement_score":0.01321979,"threshold_uncertainty_score":0.04422462,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.007476035102752699,"score_gpt":0.1913940360244631,"score_spread":0.1839180009217104,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}