{"id":"W4255166083","doi":"10.1016/j.nmd.2020.08.089","title":"SMA - CLINICAL","year":2020,"lang":"en","type":"article","venue":"Neuromuscular Disorders","topic":"Neurogenetic and Muscular Disorders Research","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"McGill University","funders":"","keywords":"SMA*; SMN1; Spinal muscular atrophy; Medicine; Cohort; Internal medicine; Retrospective cohort study; Pediatrics; Neuromuscular disease; Motor neuron; Pathophysiology; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001716516,0.0002065256,0.0003837768,0.0000617922,0.00008486368,0.00002589399,0.0002163964,0.0001163884,0.0005001378],"category_scores_gemma":[0.0005563257,0.0001881006,0.0005377106,0.000411418,0.0001997472,0.00004821691,0.000124194,0.0005172992,0.0005623544],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000007217098,"about_ca_system_score_gemma":0.0001378552,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00001056084,"about_ca_topic_score_gemma":0.000004836782,"domain_scores_codex":[0.9978309,0.0001815555,0.0003811133,0.0006306699,0.0005573398,0.0004183822],"domain_scores_gemma":[0.9987209,0.00005833868,0.00004807212,0.0004670851,0.00006123849,0.0006443855],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"not_applicable","study_design_scores_codex":[0.001109911,0.001858721,0.5004309,0.0006322232,0.0006740176,0.0007039628,0.0005426924,0.00007882911,0.01247865,0.0009759465,0.04357387,0.4369403],"study_design_scores_gemma":[0.005326449,0.001931015,0.2541313,0.00001940054,0.0002057291,0.00004176686,0.0001701313,0.001921648,0.0004571766,0.0001756764,0.7352498,0.0003698976],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9377898,0.001199651,0.001962696,0.03855082,0.0002444173,0.001113985,0.000004487135,0.0002936492,0.01884047],"genre_scores_gemma":[0.9831167,0.00177926,0.0004673318,0.01406208,0.0002114053,0.00002700083,0.00002180696,0.00007725911,0.0002371826],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.691676,"threshold_uncertainty_score":0.7670521,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.07216480188402001,"score_gpt":0.363305804387009,"score_spread":0.291141002502989,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}