{"id":"W4281674458","doi":"10.1016/j.hrthm.2022.05.030","title":"A dangerous dance: Recurrent cardiac crises in TANGO2-deficiency disorder","year":2022,"lang":"en","type":"letter","venue":"Heart Rhythm","topic":"Cardiac electrophysiology and arrhythmias","field":"Medicine","cited_by":5,"is_retracted":false,"has_abstract":false,"ca_institutions":"BC Children's Hospital; University of Alberta; University of British Columbia","funders":"University of British Columbia","keywords":"Medicine; Long QT syndrome; Internal medicine; Catecholaminergic polymorphic ventricular tachycardia; Cardiology; Short QT syndrome; QT interval; Ryanodine receptor 2","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0007526919,0.001169343,0.001238887,0.001023644,0.002230657,0.001804436,0.001077564,0.02099601,0.002746186],"category_scores_gemma":[0.01054441,0.0005364834,0.001097203,0.0006296562,0.001468551,0.001853618,0.0008964741,0.01227514,0.001261485],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.002204095,"about_ca_system_score_gemma":0.0009907646,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003441465,"about_ca_topic_score_gemma":0.004361268,"domain_scores_codex":[0.9991751,0.0002226876,0.0001388014,0.0001552233,0.000134772,0.0001734598],"domain_scores_gemma":[0.997591,0.001179333,0.0002712892,0.00009082284,0.000210294,0.0006572838],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0001005964,0.00003877197,0.006594907,0.00005927347,0.00003061111,0.9282882,0.000349629,0.0001522509,0.000512532,0.001315914,0.05903265,0.003524728],"study_design_scores_gemma":[0.0001511589,0.0001318951,0.008159947,0.0003034997,0.00006497686,0.9512341,0.001066121,0.001808791,0.0002774464,0.005802404,0.03092327,0.00007642096],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"commentary","genre_gemma":"empirical","genre_scores_codex":[0.08863784,0.007940738,0.001309491,0.8481341,0.01875835,0.0001354668,0.0003444478,0.000211725,0.03452787],"genre_scores_gemma":[0.5240319,0.005566201,0.002515833,0.3594472,0.09302358,0.0001274275,0.0002191434,0.0001984354,0.01487024],"genre_candidate":"empirical","genre_consensus":null,"teacher_disagreement_score":0.02099601,"threshold_uncertainty_score":0.01599187,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01603471264850441,"score_gpt":0.2774716840811489,"score_spread":0.2614369714326445,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}