{"id":"W4285137799","doi":"10.1177/20543581221100288","title":"Complement-Amplifying Conditions in Atypical Hemolytic Uremic Syndrome: A Canadian Case Series","year":2022,"lang":"en","type":"article","venue":"Canadian Journal of Kidney Health and Disease","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université Laval; Foothills Medical Centre; Queen's University; Hôtel-Dieu de Québec; University of Calgary; St. Michael's Hospital; University of Toronto","funders":"","keywords":"Atypical hemolytic uremic syndrome; Medicine; Alternative complement pathway; Complement system; Eculizumab; Immunology; CD46; Pathogenesis; Classical complement pathway; Complement (music); Thrombotic microangiopathy; Disease; Antibody; Internal medicine; Genetics; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["insufficient_payload"],"consensus_categories":[],"category_scores_codex":[0.0003794035,0.0001533352,0.0003275151,0.0007657339,0.001254191,0.00003225543,0.0001875864,0.0000336429,0.003704932],"category_scores_gemma":[0.002125355,0.000170891,0.00008001435,0.0002330981,0.0001490885,0.0001179331,0.00003437061,0.0003694835,0.00001429616],"about_ca_system_candidate":true,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0009878584,"about_ca_system_score_gemma":0.07220448,"about_ca_topic_candidate":true,"about_ca_topic_consensus":true,"about_ca_topic_score_codex":0.2074523,"about_ca_topic_score_gemma":0.3738178,"domain_scores_codex":[0.9980071,0.0004071324,0.0006043668,0.0001920033,0.00006043548,0.0007289681],"domain_scores_gemma":[0.9852093,0.00006599415,0.0002032029,0.0001810507,0.00005967097,0.01428072],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.000252802,0.00007071236,0.2997671,0.0002616036,0.00008221919,0.02346884,0.0009634911,0.00004068687,0.00002602619,0.001953085,0.6729009,0.0002125514],"study_design_scores_gemma":[0.005953119,0.0009796524,0.0358834,0.0005539882,0.0001363475,0.1307916,0.01333762,0.0000259638,0.000003145447,0.002377173,0.8093328,0.0006251701],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9033763,0.01352575,0.000006627798,0.07133942,0.001116288,0.0007070269,0.009824836,0.00001156477,0.00009219482],"genre_scores_gemma":[0.9728454,0.00001683125,0.00001443509,0.02637246,0.00002221607,0.0000388266,0.0005788462,0.00001424311,0.00009670492],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.2638837,"threshold_uncertainty_score":0.9972058,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02398096803608772,"score_gpt":0.2783194165584962,"score_spread":0.2543384485224084,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}