{"id":"W4291020039","doi":"10.1212/wnl.0000000000200828","title":"Frequency and Longitudinal Course of Motor Signs in Genetic Frontotemporal Dementia","year":2022,"lang":"en","type":"article","venue":"Neurology","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":11,"is_retracted":false,"has_abstract":true,"ca_institutions":"Health Sciences Centre; McGill University Health Centre; University of Toronto; Sunnybrook Health Science Centre; Western University","funders":"Janssen Pharmaceuticals; Bayer Vital; Neuraxpharm; Canadian Institutes of Health Research; Weston Brain Institute; Junta de Andalucía; Eisai; Ministero della Salute; Brain Research UK; Deutsche Forschungsgemeinschaft; NIHR Cambridge Biomedical Research Centre; European Commission; Ministerio de Ciencia e Innovación; National Institute for Health and Care Research; Ionis Pharmaceuticals; Medical Research Council; Biogen","keywords":"C9orf72; Frontotemporal dementia; Amyotrophic lateral sclerosis; Progressive supranuclear palsy; Corticobasal degeneration; Atrophy; Dementia; Psychology; Medicine; Pathology; Disease","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005672362,0.000211106,0.0001837558,0.0006935225,0.0003895948,0.000326227,0.0002721964,0.0005243696,0.001410734],"category_scores_gemma":[0.001525933,0.0001628196,0.0002979445,0.0007109962,0.0001884764,0.0003164635,0.0003561105,0.0003744042,0.000221512],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003447089,"about_ca_system_score_gemma":0.0002442337,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.01440322,"about_ca_topic_score_gemma":0.01500479,"domain_scores_codex":[0.999768,0.00005372521,0.00002189084,0.00007912564,0.00002954434,0.00004773664],"domain_scores_gemma":[0.9991958,0.0001452892,0.0003662746,0.00006088581,0.00008779908,0.0001440388],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002698776,0.00003371745,0.9979506,0.000003562694,0.0000343985,0.0000986577,0.00006040344,0.00004483528,0.0003372023,0.000008755608,0.00007215219,0.001085854],"study_design_scores_gemma":[0.000003179783,0.00004055283,0.9995516,0.000001461771,0.000009719249,0.0001377794,0.00004480454,0.0001162605,0.00004095298,0.00001426793,0.00003775282,0.000001581628],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.999393,0.00007512933,0.00005013047,0.00001360052,0.000001683566,0.000002773146,0.0003351637,0.000003126388,0.000125412],"genre_scores_gemma":[0.9993802,0.00002913892,0.00008444711,0.00000673879,0.000002801521,0.000005640407,0.0003759883,0.000001359634,0.0001135333],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01440322,"threshold_uncertainty_score":0.02863878,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0287541466817462,"score_gpt":0.288174762084381,"score_spread":0.2594206154026348,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}