{"id":"W4292791710","doi":"10.1016/j.jbspin.2022.105448","title":"Use of the Auto-inflammatory Disease Activity Index to monitor disease activity in patients with colchicine-resistant Familial Mediterranean Fever, Mevalonate Kinase Deficiency, and TRAPS treated with canakinumab","year":2022,"lang":"en","type":"article","venue":"Joint Bone Spine","topic":"Inflammasome and immune disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":10,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Montréal; Alberta Children's Hospital; Centre Hospitalier Universitaire Sainte-Justine","funders":"Swedish Orphan Biovitrum; AbbVie; Sanofi; Novartis Pharma; Roche; Novartis","keywords":"Medicine; Familial Mediterranean fever; Canakinumab; Internal medicine; Disease; Colchicine; Gastroenterology; Anakinra","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001334116,0.0004481362,0.0006902793,0.0005139783,0.0002111843,0.0004599587,0.0001979661,0.0002900649,0.0005013155],"category_scores_gemma":[0.002481568,0.0001396899,0.000389462,0.0003532867,0.0001816116,0.0003385944,0.0002669957,0.0004090639,0.0001428489],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000189672,"about_ca_system_score_gemma":0.000197548,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000512718,"about_ca_topic_score_gemma":0.0007880984,"domain_scores_codex":[0.9990836,0.0004387783,0.0000992739,0.0001404756,0.0001682992,0.00006946064],"domain_scores_gemma":[0.9983102,0.0005025545,0.0006620011,0.00008369256,0.0001758201,0.0002657432],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.003681972,0.0001949769,0.9844654,0.00003174469,0.0001552252,0.00007183431,0.00007031369,0.0002487496,0.002416691,0.00001074587,0.00007647342,0.008575828],"study_design_scores_gemma":[0.0002197907,0.003282923,0.9930467,0.00001317149,0.0001049386,0.0004006186,0.00006455379,0.001715875,0.0008585127,0.00001286107,0.0002698158,0.00001028514],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9986803,0.0004881258,0.0002535141,0.00002294615,0.000007686011,0.00003870042,0.00008083664,0.000006424672,0.0004214394],"genre_scores_gemma":[0.999391,0.00006767919,0.000312283,0.00001777616,0.00001074593,0.00002328528,0.0001151778,0.000001023211,0.00006117624],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001334116,"threshold_uncertainty_score":0.007055581,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.007965344436664879,"score_gpt":0.1995293946075613,"score_spread":0.1915640501708964,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}