{"id":"W4300818840","doi":"10.1002/ppul.26173","title":"Respiratory characteristics in children with spinal muscular atrophy type 1 receiving nusinersen","year":2022,"lang":"en","type":"article","venue":"Pediatric Pulmonology","topic":"Neurogenetic and Muscular Disorders Research","field":"Medicine","cited_by":12,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Alberta; Stollery Children's Hospital; Hospital for Sick Children; University of Toronto","funders":"","keywords":"Medicine; Polysomnography; Polysomnogram; Interquartile range; Neuromuscular disease; Apnea; Pediatrics; Respiratory failure; Central sleep apnea; Physical therapy; Anesthesia; Internal medicine; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005216032,0.0002930452,0.0004434401,0.001123593,0.0006674277,0.0006486526,0.000459896,0.0004938631,0.001525858],"category_scores_gemma":[0.001969558,0.0002295146,0.0006077323,0.001711931,0.0004190141,0.0004745364,0.0006037523,0.0006315411,0.0001886915],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001591268,"about_ca_system_score_gemma":0.00121088,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0530553,"about_ca_topic_score_gemma":0.07410662,"domain_scores_codex":[0.9994226,0.00005388775,0.00007056105,0.0001228059,0.0001478052,0.0001823952],"domain_scores_gemma":[0.9982869,0.0001726096,0.0009561902,0.00004599672,0.0001954543,0.0003428567],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00001503077,0.000004095838,0.9996799,0.000004242624,0.000004916032,0.0000639881,0.00004167265,0.000007826678,0.00002682239,0.000002714678,0.00002547342,0.0001233462],"study_design_scores_gemma":[0.000001238936,0.00005089767,0.9991775,0.000008119842,0.000004923956,0.0003823656,0.0002659512,0.00002009529,0.00001417786,0.000002807143,0.00007016795,0.000001731822],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9985732,0.0002723192,0.00001664393,0.00003070269,0.000004258922,0.00001164424,0.0008234179,0.000001918283,0.0002658826],"genre_scores_gemma":[0.9987482,0.000171473,0.00004299676,0.00003066493,0.000005496567,0.00001130547,0.000916525,0.00000139707,0.00007207267],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0530553,"threshold_uncertainty_score":0.1054929,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01666710304231685,"score_gpt":0.2712609088378647,"score_spread":0.2545938057955479,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}