{"id":"W4307023903","doi":"10.1016/j.cjca.2022.08.109","title":"EARLY DETECTION OF POLYNEUROPATHY IN PATIENTS WITH HEREDITARY TRANSTHYRETIN AMYLOIDOSIS CARDIOMYOPATHY","year":2022,"lang":"en","type":"article","venue":"Canadian Journal of Cardiology","topic":"Amyloidosis: Diagnosis, Treatment, Outcomes","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"The Scarborough Hospital","funders":"","keywords":"Medicine; Polyneuropathy; Neurology; Neurological examination; Cardiomyopathy; Transthyretin; Amyloidosis; Physical examination; Disease; Pediatrics; Internal medicine; Cardiac amyloidosis; Surgery; Heart failure","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005270158,0.0005394816,0.0009461169,0.0008398459,0.0008183733,0.001046402,0.000451104,0.001507308,0.001627786],"category_scores_gemma":[0.003864771,0.0002951383,0.0005397499,0.0008312014,0.000334704,0.0007692637,0.0004632408,0.001529993,0.0002458135],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006847092,"about_ca_system_score_gemma":0.0009118479,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.006601138,"about_ca_topic_score_gemma":0.007282725,"domain_scores_codex":[0.9994221,0.0001162873,0.00005271417,0.00008130699,0.0001411444,0.0001864611],"domain_scores_gemma":[0.9976074,0.0007461795,0.000561415,0.00006176757,0.0003883542,0.0006347929],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003696074,0.0002252315,0.9923744,0.00003317725,0.0000253064,0.001291056,0.00007464312,0.00005999248,0.0003097686,0.00002261694,0.0002873702,0.004926867],"study_design_scores_gemma":[0.00002680192,0.0004841696,0.9933025,0.00006844057,0.00007144158,0.004698756,0.0003652695,0.0003528652,0.0001658909,0.0001455294,0.0002972594,0.00002109174],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9939346,0.002441357,0.0001716111,0.000715744,0.00007480141,0.00002128066,0.0001914657,0.00001462563,0.002434599],"genre_scores_gemma":[0.9984248,0.00063765,0.0001272283,0.0001457407,0.0001085709,0.000008037986,0.0002187389,0.000002487574,0.0003268025],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.006601138,"threshold_uncertainty_score":0.01312542,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.004059066812463936,"score_gpt":0.179881790016781,"score_spread":0.1758227232043171,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}