{"id":"W4308364421","doi":"10.1001/jamaneurol.2022.3791","title":"Slowly Progressive Cerebellar Ataxia in a 55-Year-Old Female Patient","year":2022,"lang":"en","type":"article","venue":"JAMA Neurology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"London Health Sciences Centre; Western University","funders":"","keywords":"Dysarthria; Cerebellar ataxia; Ataxia; Nystagmus; Medicine; Cerebellum; Audiology; Neurological examination; Atrophy; Psychology; Falling (accident); Anxiety; Physical medicine and rehabilitation; Neuroscience; Pathology; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001041742,0.0002308906,0.0002494124,0.0002134188,0.0002604826,0.00004598746,0.0005358586,0.00007536428,0.0008835073],"category_scores_gemma":[0.000675626,0.0002451597,0.00008980707,0.0005728492,0.0001739596,0.00008693427,0.0007542155,0.0007353146,0.0001653944],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0000345039,"about_ca_system_score_gemma":0.00009433852,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00002228141,"about_ca_topic_score_gemma":0.00001109812,"domain_scores_codex":[0.9962635,0.001369423,0.0003408311,0.0009788864,0.00045984,0.0005875312],"domain_scores_gemma":[0.9988232,0.0002958185,0.0001750245,0.0005357729,0.00003377888,0.0001363771],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.002604424,0.002870896,0.2074994,0.00006365621,0.00001557444,0.009325439,0.00300131,0.01288838,0.7250109,0.005398221,0.02245417,0.008867672],"study_design_scores_gemma":[0.004561939,0.005386447,0.1147241,0.000007911314,0.0000325049,0.0007338752,0.000261336,0.002341591,0.7659907,0.001722239,0.1032508,0.0009866133],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9950516,0.0001235082,0.000003354259,0.002138573,0.0006658158,0.0006668046,0.0001176979,0.00007910425,0.001153558],"genre_scores_gemma":[0.9817041,0.00001369958,0.00004139926,0.01740553,0.00008301449,0.0004517089,0.000008516411,0.00004488256,0.0002471663],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.09277534,"threshold_uncertainty_score":0.9997323,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0187260689464428,"score_gpt":0.2471260111497745,"score_spread":0.2283999422033317,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}