{"id":"W4309115043","doi":"10.1002/rth2.12840","title":"Hereditary thrombotic thrombocytopenic purpura: The risk for death at birth","year":2022,"lang":"en","type":"article","venue":"Research and Practice in Thrombosis and Haemostasis","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":4,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Thrombotic thrombocytopenic purpura; Medicine; Purpura (gastropod); Thrombocytopenic purpura; Pediatrics; Immunology; Intensive care medicine; Platelet; Biology","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002466182,0.0004466652,0.0005675934,0.001058664,0.0007710151,0.0005991523,0.0003074865,0.001221633,0.01252714],"category_scores_gemma":[0.002466193,0.0001519159,0.0003708443,0.001101713,0.0002511485,0.0007007982,0.0006285773,0.00130238,0.00161585],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002796185,"about_ca_system_score_gemma":0.0003146611,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002298308,"about_ca_topic_score_gemma":0.001230627,"domain_scores_codex":[0.9997568,0.0000512991,0.00001263862,0.0000545771,0.00007610187,0.00004860029],"domain_scores_gemma":[0.9993986,0.0001103702,0.0002021123,0.00004086935,0.00009206661,0.0001560301],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0007132931,0.00022136,0.7704912,0.0007089663,0.000584365,0.01475472,0.0007479904,0.0003127068,0.003095132,0.008849842,0.04860076,0.1509196],"study_design_scores_gemma":[0.00005294617,0.0002740052,0.8623257,0.00169049,0.0006605582,0.08081844,0.000666454,0.0004912453,0.001005131,0.01100287,0.04093421,0.00007795783],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.8290011,0.06635755,0.00389193,0.01808733,0.001522162,0.00009986794,0.0131143,0.0004834899,0.06744225],"genre_scores_gemma":[0.9506457,0.02992222,0.001794393,0.001207784,0.0005617457,0.00008124442,0.003112625,0.00005995331,0.0126143],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01252714,"threshold_uncertainty_score":0.04190743,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1967242816533027,"score_gpt":0.4255967783550418,"score_spread":0.228872496701739,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}