{"id":"W4309149093","doi":"10.1007/s00415-022-11442-y","title":"Motor symptoms in genetic frontotemporal dementia: developing a new module for clinical rating scales","year":2022,"lang":"en","type":"article","venue":"Journal of Neurology","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":18,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Western University; Montreal Neurological Institute and Hospital; University of Toronto; Occupational Cancer Research Centre; Health Sciences Centre; McGill University Health Centre; Sunnybrook Health Science Centre; Université Laval","funders":"NIHR Cambridge Biomedical Research Centre; Instituto de Salud Carlos III; Medical Research Council; UK Dementia Research Institute; Stichting Dioraphte; Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico; Fondazione I.R.C.C.S. Istituto Neurologico Carlo Besta; Universiteit Antwerpen; University of Toronto; Universidade de Coimbra; Università degli Studi di Brescia; Robarts Research Institute; Alzheimer's Society; Ministero della Salute; Toronto Rehabilitation Institute; Centro de Investigación Biomédica en Red sobre Enfermedades Neurodegenerativas; Wolfson Foundation; Wellcome Trust; University College London; National Institute for Health and Care Research; Brain Research UK; Alzheimer's Research Trust; National Brain Appeal; Nederlandse Organisatie voor Wetenschappelijk Onderzoek; Erasmus Medisch Centrum; Deutsche Forschungsgemeinschaft; University Health Network; Università degli Studi di Milano; EU Joint Programme – Neurodegenerative Disease Research; Sunnybrook Research Institute; Fundació la Marató de TV3; Weston Brain Institute; Canadian Institutes of Health Research; London School of Hygiene and Tropical Medicine","keywords":"Frontotemporal dementia; C9orf72; Clinical Dementia Rating; Parkinsonism; Frontotemporal lobar degeneration; Rating scale; Amyotrophic lateral sclerosis; Dementia; Psychology; Medicine; Dysarthria; Physical medicine and rehabilitation; Executive dysfunction; Internal medicine; Psychiatry; Neuropsychology; Disease; Cognition","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.01943988,0.001157296,0.00161739,0.002423013,0.0003273573,0.001361619,0.001500535,0.0009529518,0.003026563],"category_scores_gemma":[0.03864698,0.0005881293,0.001495808,0.001130858,0.0003119293,0.002107139,0.001678485,0.001233831,0.001492137],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006951987,"about_ca_system_score_gemma":0.0009059143,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001284112,"about_ca_topic_score_gemma":0.00173576,"domain_scores_codex":[0.9900258,0.005414692,0.001616436,0.0004807974,0.002141665,0.0003206735],"domain_scores_gemma":[0.9770966,0.01447402,0.0019521,0.0009159257,0.004892532,0.0006687461],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"observational","study_design_scores_codex":[0.004163722,0.002008522,0.4494134,0.0007018612,0.0008832102,0.0002056423,0.0008368332,0.005116547,0.004884663,0.001021059,0.01075479,0.5200099],"study_design_scores_gemma":[0.001663042,0.005270805,0.9154576,0.0003871784,0.0003760136,0.001176431,0.0006342198,0.05826585,0.002939313,0.002032704,0.01159013,0.0002066694],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.7993854,0.002702106,0.1549197,0.0009123133,0.0005730279,0.01751621,0.006941425,0.002697085,0.01435273],"genre_scores_gemma":[0.6378216,0.0009553559,0.3243107,0.0003442556,0.0002810582,0.02521001,0.007174941,0.0002995141,0.003602638],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01943988,"threshold_uncertainty_score":0.1028092,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.08887819727129036,"score_gpt":0.3870390844662779,"score_spread":0.2981608871949876,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}