{"id":"W4309149093","doi":"10.1007/s00415-022-11442-y","title":"Motor symptoms in genetic frontotemporal dementia: developing a new module for clinical rating scales","year":2022,"lang":"en","type":"article","venue":"Journal of Neurology","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":18,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Western University; Montreal Neurological Institute and Hospital; University of Toronto; Occupational Cancer Research Centre; Health Sciences Centre; McGill University Health Centre; Sunnybrook Health Science Centre; Université Laval","funders":"NIHR Cambridge Biomedical Research Centre; Instituto de Salud Carlos III; Medical Research Council; UK Dementia Research Institute; Stichting Dioraphte; Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico; Fondazione I.R.C.C.S. Istituto Neurologico Carlo Besta; Universiteit Antwerpen; University of Toronto; Universidade de Coimbra; Università degli Studi di Brescia; Robarts Research Institute; Alzheimer's Society; Ministero della Salute; Toronto Rehabilitation Institute; Centro de Investigación Biomédica en Red sobre Enfermedades Neurodegenerativas; Wolfson Foundation; Wellcome Trust; University College London; National Institute for Health and Care Research; Brain Research UK; Alzheimer's Research Trust; National Brain Appeal; Nederlandse Organisatie voor Wetenschappelijk Onderzoek; Erasmus Medisch Centrum; Deutsche Forschungsgemeinschaft; University Health Network; Università degli Studi di Milano; EU Joint Programme – Neurodegenerative Disease Research; Sunnybrook Research Institute; Fundació la Marató de TV3; Weston Brain Institute; Canadian Institutes of Health Research; London School of Hygiene and Tropical Medicine","keywords":"Frontotemporal dementia; C9orf72; Clinical Dementia Rating; Parkinsonism; Frontotemporal lobar degeneration; Rating scale; Amyotrophic lateral sclerosis; Dementia; Psychology; Medicine; Dysarthria; Physical medicine and rehabilitation; Executive dysfunction; Internal medicine; Psychiatry; Neuropsychology; Disease; Cognition","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0008636079,0.00009492203,0.000440934,0.0001933447,0.00008443995,0.00001087894,0.0002067836,0.00007688642,0.0001131934],"category_scores_gemma":[0.0003861177,0.00008056971,0.0001689409,0.0001314353,0.00004994056,0.0000578553,0.0001691399,0.0007619389,0.000002061877],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00008332241,"about_ca_system_score_gemma":0.00043771,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00002964326,"about_ca_topic_score_gemma":0.00002297427,"domain_scores_codex":[0.9978904,0.0003455526,0.0009057253,0.0001904923,0.0003485802,0.0003192514],"domain_scores_gemma":[0.9990427,0.0002567616,0.0003192994,0.0001199439,0.00009532196,0.0001659034],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00273513,0.0001753515,0.9726396,0.00002750533,0.0001528884,0.000560772,0.00007550921,0.0005034595,0.003704719,0.00003025603,0.003898832,0.01549595],"study_design_scores_gemma":[0.004422467,0.004956505,0.9791504,0.00001687845,0.00004006572,0.0006986502,0.00001037771,0.004193716,0.0000110185,0.0004396707,0.005992323,0.00006797657],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9815859,0.0007641561,0.00266153,0.01418625,0.0004549387,0.0003262477,0.000001874761,0.000006417092,0.00001264464],"genre_scores_gemma":[0.9853029,0.0001079914,0.01130595,0.00253328,0.0006272262,0.00001653579,0.000001495652,0.00002213583,0.00008253535],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01542797,"threshold_uncertainty_score":0.3310288,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.08887819727129036,"score_gpt":0.3870390844662779,"score_spread":0.2981608871949876,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}