{"id":"W4309905690","doi":"10.3389/fnhum.2022.1006115","title":"Brain arteriovenous malformation in hereditary hemorrhagic telangiectasia: Recent advances in cellular and molecular mechanisms","year":2022,"lang":"en","type":"review","venue":"Frontiers in Human Neuroscience","topic":"Vascular Anomalies and Treatments","field":"Medicine","cited_by":24,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hôpital Maisonneuve-Rosemont; Université de Montréal; Centre Hospitalier Universitaire Sainte-Justine","funders":"Fonds de Recherche du Québec - Santé; Canadian Institutes of Health Research; Université de Montréal","keywords":"Telangiectasia; Endoglin; ACVRL1; Arteriovenous malformation; Medicine; Pathogenesis; Notch signaling pathway; Pathology; Cancer research; Biology; Receptor; Internal medicine; Cell biology; Surgery; Stem cell","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005954394,0.0005577349,0.0007134342,0.00130258,0.0002069309,0.0007897667,0.0005375177,0.0009782517,0.001587496],"category_scores_gemma":[0.0004077272,0.0001974727,0.0004289135,0.001109886,0.0007621657,0.001165939,0.0005061472,0.001303738,0.0004271259],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005009481,"about_ca_system_score_gemma":0.0006693383,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0008788192,"about_ca_topic_score_gemma":0.0007384088,"domain_scores_codex":[0.9998627,0.00002690008,0.00002171194,0.00003684467,0.00002981804,0.00002203036],"domain_scores_gemma":[0.9996654,0.0001175808,0.00006860174,0.00001979021,0.00007915087,0.00004950523],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0006172766,0.0003288243,0.005224315,0.01188664,0.0002806376,0.003001144,0.0002643798,0.0009731433,0.04128762,0.01116055,0.01293441,0.9120411],"study_design_scores_gemma":[0.0002084965,0.001192257,0.03537309,0.003329593,0.002131517,0.03931966,0.0006040483,0.003963809,0.04231365,0.02122773,0.8501263,0.0002099224],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.006102596,0.9884388,0.001840774,0.001530875,0.0002186546,0.000009357789,0.00005549304,0.00004212048,0.001761325],"genre_scores_gemma":[0.03630714,0.9583757,0.00243183,0.000617433,0.001132935,0.00002255108,0.0001616074,0.000007323232,0.0009435907],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.001587496,"threshold_uncertainty_score":0.005310774,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01994321221230232,"score_gpt":0.2807586701502414,"score_spread":0.260815457937939,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}