{"id":"W4311976721","doi":"10.1007/s00415-022-11512-1","title":"Language impairment in the genetic forms of behavioural variant frontotemporal dementia","year":2022,"lang":"en","type":"article","venue":"Journal of Neurology","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":13,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Western University; Montreal Neurological Institute and Hospital; University of Toronto; Occupational Cancer Research Centre; Health Sciences Centre; McGill University Health Centre; Sunnybrook Health Science Centre; Université Laval","funders":"NIHR Cambridge Biomedical Research Centre; Instituto de Salud Carlos III; Medical Research Council; Tau Consortium; UK Dementia Research Institute; Stichting Dioraphte; Networks of Centres of Excellence of Canada; Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico; Fondazione I.R.C.C.S. Istituto Neurologico Carlo Besta; Università degli Studi di Brescia; Stockholms Läns Landsting; Universidade de Coimbra; University of Toronto; Nederlandse Organisatie voor Wetenschappelijk Onderzoek; Alzheimer's Society; Alzheimer Society; Ministero della Salute; Toronto Rehabilitation Institute; Centro de Investigación Biomédica en Red sobre Enfermedades Neurodegenerativas; Wolfson Foundation; Wellcome Trust; University College London; University of Cambridge; Bundesministerium für Bildung und Forschung; National Institute for Health and Care Research; Karolinska Institutet; Weston Brain Institute; ZonMw; Brain Research UK; Alzheimer's Research Trust; National Brain Appeal; Agence Nationale de la Recherche; Deutsche Forschungsgemeinschaft; University Health Network; Università degli Studi di Milano; EU Joint Programme – Neurodegenerative Disease Research; Alzheimer Nederland; Sunnybrook Research Institute; Fundació la Marató de TV3; Canadian Institutes of Health Research; London School of Hygiene and Tropical Medicine","keywords":"Frontotemporal dementia; Psychology; Primary progressive aphasia; Audiology; Boston Naming Test; C9orf72; Verbal fluency test; Aphasia; Fluency; Dementia; Neuropsychology; Cognitive psychology; Medicine; Pathology; Neuroscience; Cognition; Disease","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004915454,0.0007753315,0.0004302569,0.001297739,0.0006516675,0.00052865,0.0003915419,0.0006564091,0.002127953],"category_scores_gemma":[0.00156038,0.0002145573,0.000222014,0.0005125568,0.0007055532,0.0004699637,0.0006164226,0.0003224814,0.0003454591],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005149981,"about_ca_system_score_gemma":0.0002389407,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.006022349,"about_ca_topic_score_gemma":0.008358296,"domain_scores_codex":[0.9997171,0.00005354478,0.00003109176,0.00007065848,0.00006856736,0.00005905089],"domain_scores_gemma":[0.999632,0.00007758909,0.0001645672,0.00001765504,0.00005197142,0.00005626228],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.002245609,0.0002800144,0.9427249,0.0001577334,0.0001439423,0.02161085,0.002040505,0.0001810552,0.01232174,0.0001695953,0.0004598658,0.01766409],"study_design_scores_gemma":[0.00002863003,0.0005717449,0.9708896,0.00004370136,0.00005260678,0.02643163,0.0006385369,0.0001392343,0.0004735495,0.0003623867,0.0003575821,0.00001069319],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9988011,0.0002608669,0.00004134342,0.00003341084,0.000003273967,0.000007758455,0.00007123195,0.00000410608,0.0007770284],"genre_scores_gemma":[0.9996276,0.00006826437,0.00005593307,0.00002240018,0.00000530744,0.000003577578,0.0000730065,0.000001263663,0.0001426831],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.006022349,"threshold_uncertainty_score":0.01197457,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03332022241091582,"score_gpt":0.2954502460422622,"score_spread":0.2621300236313464,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}