{"id":"W4316814611","doi":"10.15690/vsp.v21i6s.2488","title":"How to Distinguish Attenuated Forms of Mucopolysaccharidosis and Articular Forms of Juvenile Arthritis: Development of Diagnostic Algorithm Based on the Data from Multicenter Retrospective Study","year":2023,"lang":"en","type":"article","venue":"Вопросы современной педиатрии","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Children’s Health Research Institute","funders":"","keywords":"Medicine; Juvenile rheumatoid arthritis; Arthritis; Internal medicine; Retrospective cohort study; Mucopolysaccharidosis; Surgery; Pediatrics","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.008783869,0.0006788423,0.001054916,0.00630394,0.000566031,0.001778894,0.0009242595,0.0005877541,0.00119449],"category_scores_gemma":[0.01880383,0.0003401683,0.0009511028,0.002633884,0.0002756292,0.001261211,0.001106569,0.0004463824,0.0003408176],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000427437,"about_ca_system_score_gemma":0.0009966039,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001896457,"about_ca_topic_score_gemma":0.002068162,"domain_scores_codex":[0.9940997,0.002232955,0.001761522,0.0009159346,0.0007173699,0.0002726591],"domain_scores_gemma":[0.9906315,0.00288889,0.002293936,0.000685176,0.002964051,0.0005365316],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001594116,0.0000384489,0.9801825,0.0001057485,0.0001349014,0.0003266383,0.0001369598,0.000261558,0.0004886313,0.000152695,0.001166733,0.01684574],"study_design_scores_gemma":[0.0001212898,0.000355572,0.9622478,0.0004585356,0.0008346271,0.005942018,0.00226385,0.01576838,0.002147974,0.001469108,0.008307023,0.00008377375],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9443825,0.00375859,0.03983366,0.001039469,0.00022083,0.001922882,0.005499371,0.0001962754,0.003146418],"genre_scores_gemma":[0.9387429,0.001076633,0.05153068,0.0001908384,0.0001494854,0.001296733,0.006739619,0.00003076626,0.0002422582],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.008783869,"threshold_uncertainty_score":0.04645407,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04108347192164748,"score_gpt":0.3055214721817993,"score_spread":0.2644380002601519,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}