{"id":"W4361027546","doi":"10.1016/j.neurol.2023.01.409","title":"Ataxie spastique de Charlevoix-Saguenay (ARSACS) : à propos d’une famille","year":2023,"lang":"fr","type":"article","venue":"Revue Neurologique","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"","keywords":"Medicine; Gynecology","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","insufficient_payload"],"consensus_categories":[],"category_scores_codex":[0.0007506675,0.000804332,0.0007228286,0.0003792924,0.0004671106,0.0001942683,0.001271652,0.0005893162,0.0003649694],"category_scores_gemma":[0.00447123,0.0008833165,0.0003944501,0.002265838,0.0007905343,0.0002871199,0.0006718962,0.001423266,0.004286621],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001296,"about_ca_system_score_gemma":0.0005855214,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000189331,"about_ca_topic_score_gemma":0.0001142194,"domain_scores_codex":[0.9917703,0.002895258,0.0007737431,0.002053722,0.0005169039,0.001990024],"domain_scores_gemma":[0.9961063,0.001285684,0.0003554875,0.001383335,0.0001792915,0.0006898851],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0002091116,0.0006393112,0.01097057,0.0008321404,0.00003305863,0.007929869,0.0009265199,0.01067205,0.9126294,0.00587959,0.04121345,0.008064975],"study_design_scores_gemma":[0.001139608,0.002334665,0.0913266,0.0002605618,0.0001775678,0.001287732,0.0001069155,0.02850155,0.7712108,0.003257683,0.09894631,0.001449995],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9397381,0.001001136,0.0007546631,0.04885279,0.00411367,0.001690433,0.0003732828,0.0008892008,0.002586726],"genre_scores_gemma":[0.9477811,0.008960688,0.0002942087,0.007970491,0.001285339,0.0004611192,0.0000330436,0.0002391376,0.0329748],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1414185,"threshold_uncertainty_score":0.9993618,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03199198094608647,"score_gpt":0.2672223608116449,"score_spread":0.2352303798655584,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}