{"id":"W4362734885","doi":"10.1016/j.ijcard.2023.04.016","title":"Clinical and CMR characteristics associated with cardiac events in patients with Fabry disease","year":2023,"lang":"en","type":"article","venue":"International Journal of Cardiology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":11,"is_retracted":false,"has_abstract":true,"ca_institutions":"Toronto General Hospital","funders":"","keywords":"Medicine; Cardiology; Internal medicine; Clinical endpoint; Atrial fibrillation; Univariate analysis; Heart failure; Sudden cardiac death; Fabry disease; Surrogate endpoint; Cardiac magnetic resonance imaging; Magnetic resonance imaging; Disease; Radiology; Clinical trial; Multivariate analysis","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0006334272,0.0002884496,0.0003671591,0.00048983,0.0002928176,0.0004485101,0.0002226185,0.0004877086,0.00115113],"category_scores_gemma":[0.002030634,0.0001352129,0.0002703384,0.0004068057,0.0002451553,0.0002993634,0.0002977077,0.0004402236,0.0001730793],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001813365,"about_ca_system_score_gemma":0.0001856094,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0005455777,"about_ca_topic_score_gemma":0.0006201929,"domain_scores_codex":[0.9997774,0.00005688849,0.00002505431,0.00005363367,0.00003919053,0.00004789139],"domain_scores_gemma":[0.9988237,0.0003219577,0.0005035851,0.00004749547,0.00007027145,0.0002329983],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002055386,0.00001937257,0.9984866,0.00000407134,0.00001362823,0.0002075257,0.00002433691,0.00004784863,0.0002275797,0.000008123379,0.00002499043,0.0007304362],"study_design_scores_gemma":[0.00001032408,0.0001668139,0.9985856,0.000004082483,0.00002033565,0.0008812145,0.00005129998,0.0001425883,0.00004389552,0.00002591642,0.00006545685,0.000002557076],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9994913,0.0002245343,0.00004689039,0.00002329099,0.000002477223,0.000003002761,0.00006124631,0.000001251012,0.0001457788],"genre_scores_gemma":[0.999741,0.00004205761,0.00003823146,0.00001318095,0.000009424683,0.000003193613,0.0001178925,4.592551e-7,0.00003458157],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.00115113,"threshold_uncertainty_score":0.003850937,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02151174241370784,"score_gpt":0.3382821456098141,"score_spread":0.3167704031961062,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}