{"id":"W4377696196","doi":"10.1016/j.clim.2023.109414","title":"Interstitial cystitis caused by immune dysregulation in LRBA deficiency: one among the rare urological manifestations in inborn errors of immunity","year":2023,"lang":"en","type":"article","venue":"Clinical Immunology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":1,"is_retracted":false,"has_abstract":false,"ca_institutions":"Dalhousie University; Hospital for Sick Children; Izaak Walton Killam Health Centre; McMaster University; McMaster Children's Hospital","funders":"","keywords":"Medicine; Immunology; Interstitial cystitis; Hypogammaglobulinemia; Autoimmunity; Pathology; Immune system; Urinary system; Internal medicine; Antibody","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","sts"],"consensus_categories":[],"category_scores_codex":[0.002206125,0.0003166974,0.0008165514,0.0004455507,0.0003028559,0.00001579784,0.000988684,0.0008710817,0.0004056574],"category_scores_gemma":[0.001638486,0.0002701914,0.000265583,0.001309779,0.003075602,0.0001945707,0.0004534257,0.001723229,0.0003520745],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00007450943,"about_ca_system_score_gemma":0.0001477078,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001832737,"about_ca_topic_score_gemma":0.0003513751,"domain_scores_codex":[0.9945437,0.001967797,0.002030441,0.000551197,0.00009023991,0.0008166314],"domain_scores_gemma":[0.9966582,0.00194118,0.0005062803,0.0007747327,0.0001082048,0.00001137348],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.003202486,0.007633186,0.394727,0.000133033,0.000994312,0.0002057104,0.01213729,0.001902725,0.5082201,0.0118535,0.001413564,0.05757714],"study_design_scores_gemma":[0.003329629,0.0006264944,0.9883035,0.00009617898,0.00004861989,0.00001759393,0.003190571,0.0001649873,0.00170652,0.001230121,0.0009937711,0.0002920506],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9862943,0.009603577,0.0001093824,0.001131414,0.001429925,0.0005895038,0.00006444564,0.0001286474,0.0006487882],"genre_scores_gemma":[0.9976608,0.000910404,0.000008302337,0.0001218496,0.000005334817,0.0001035591,0.0007162618,0.00002686434,0.0004466248],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.5935765,"threshold_uncertainty_score":0.999975,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03089629090599562,"score_gpt":0.2983907825699955,"score_spread":0.2674944916639999,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}