{"id":"W4384616215","doi":"10.1080/13506129.2023.2229484","title":"Patients with transthyretin amyloidosis enrolled in THAOS between 2018 and 2021 continue to experience substantial diagnostic delay","year":2023,"lang":"en","type":"article","venue":"Amyloid","topic":"Amyloidosis: Diagnosis, Treatment, Outcomes","field":"Biochemistry, Genetics and Molecular Biology","cited_by":14,"is_retracted":false,"has_abstract":true,"ca_institutions":"Foothills Medical Centre; University of Alberta","funders":"Daiichi Sankyo Europe; VA Greater Los Angeles Healthcare System; University of California, Irvine; School of Medicine, Vanderbilt University; Aarhus Universitet; Fleni; Università degli Studi di Messina; Samsung; Konkuk University; Cleveland Clinic; Chiba University; RWTH Aachen University; Alnylam Pharmaceuticals; National Taiwan University; National Taiwan University Hospital; Konkuk University Medical Center; Prothena; Boston Scientific Corporation; Temple University; Sanofi; Sungkyunkwan University; Cleveland Clinic Foundation; Pfizer; University of Miami; Celgene; University of Pennsylvania; Vanderbilt University; Aarhus Universitetshospital","keywords":"Transthyretin; Amyloidosis; Medicine; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002512165,0.0001543606,0.0002513044,0.0003682433,0.0006594829,0.001017247,0.0002196832,0.0004137428,0.003900561],"category_scores_gemma":[0.002846728,0.00007569203,0.000238917,0.0009732002,0.0001843664,0.0008126113,0.0004571874,0.0007003804,0.0007167647],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004439073,"about_ca_system_score_gemma":0.001073617,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.01108728,"about_ca_topic_score_gemma":0.01529752,"domain_scores_codex":[0.9996932,0.00003203827,0.00003624901,0.00005595237,0.00007182316,0.0001108171],"domain_scores_gemma":[0.9991862,0.0001478716,0.0003243986,0.00001470703,0.00008616602,0.0002407943],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002006015,0.00003679459,0.9625739,0.00003440945,0.0000236696,0.001250987,0.0003956206,0.00004356131,0.0004512088,0.0002626437,0.006145924,0.02858068],"study_design_scores_gemma":[0.00002481895,0.000081701,0.977325,0.0001329219,0.00004975167,0.004161324,0.003279845,0.0002139657,0.0002278265,0.0004415404,0.01404521,0.00001600859],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9721639,0.004813069,0.0002451747,0.007220785,0.0008266162,0.00001933429,0.002162474,0.00005575441,0.01249281],"genre_scores_gemma":[0.992226,0.002950357,0.0002008825,0.00125939,0.0003482657,0.00001542849,0.001184709,0.00001130314,0.00180371],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01108728,"threshold_uncertainty_score":0.02204549,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.008007715474747445,"score_gpt":0.2442142379450165,"score_spread":0.236206522470269,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}