{"id":"W4385564577","doi":"10.1002/ppul.26554","title":"Duchenne muscular dystrophy respiratory profiles from real world registry data","year":2023,"lang":"en","type":"article","venue":"Pediatric Pulmonology","topic":"Muscle Physiology and Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":5,"is_retracted":false,"has_abstract":true,"ca_institutions":"Children’s Health Research Institute; London Health Sciences Centre; Western University","funders":"Academic Medical Organization of Southwestern Ontario","keywords":"Medicine; Duchenne muscular dystrophy; Vital capacity; Pulmonary function testing; Physical therapy; Population; Neuromuscular disease; Cohort; Scoliosis; Pediatrics; Disease; Internal medicine; Surgery; Lung; Lung function; Diffusing capacity","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002403179,0.000235522,0.0002603937,0.0001873585,0.0001335054,0.00001510204,0.0009470278,0.0003594091,0.00009069488],"category_scores_gemma":[0.0002650122,0.0002394215,0.00008680364,0.0004613273,0.0001673964,0.00001069067,0.0008173494,0.0002387352,0.0002960188],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000011809,"about_ca_system_score_gemma":0.0001822206,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0003580038,"about_ca_topic_score_gemma":0.0002326443,"domain_scores_codex":[0.9979091,0.0001769778,0.0003153057,0.000970543,0.0001117833,0.0005163024],"domain_scores_gemma":[0.9978861,0.00005867026,0.0001559626,0.001732707,0.00005174531,0.0001148565],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"observational","study_design_scores_codex":[0.001022256,0.0003480995,0.3271428,0.0001224594,0.0003853678,0.0002397048,0.00006652984,0.0001930826,0.2739849,0.000558986,0.3868447,0.009091129],"study_design_scores_gemma":[0.002621141,0.000650641,0.6120444,0.00001216837,0.0003198185,0.000009483473,0.0002090266,0.0003703426,0.006105271,0.004627513,0.3716539,0.001376241],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9948285,0.002117138,0.00007956167,0.0003845259,0.0005484505,0.0001892253,0.0003378338,0.000123934,0.00139086],"genre_scores_gemma":[0.9873149,0.003288863,0.0003257375,0.0004434981,0.002670515,0.00007683224,0.00510667,0.00004814165,0.0007248807],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.2849016,"threshold_uncertainty_score":0.9763324,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03118785973395963,"score_gpt":0.2847769805860794,"score_spread":0.2535891208521197,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}