{"id":"W4385564577","doi":"10.1002/ppul.26554","title":"Duchenne muscular dystrophy respiratory profiles from real world registry data","year":2023,"lang":"en","type":"article","venue":"Pediatric Pulmonology","topic":"Muscle Physiology and Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":5,"is_retracted":false,"has_abstract":true,"ca_institutions":"Children’s Health Research Institute; London Health Sciences Centre; Western University","funders":"Academic Medical Organization of Southwestern Ontario","keywords":"Medicine; Duchenne muscular dystrophy; Vital capacity; Pulmonary function testing; Physical therapy; Population; Neuromuscular disease; Cohort; Scoliosis; Pediatrics; Disease; Internal medicine; Surgery; Lung; Lung function; Diffusing capacity","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.005024388,0.000338083,0.0006047411,0.002813185,0.0005925123,0.001245971,0.001000569,0.0003766149,0.001976982],"category_scores_gemma":[0.01467554,0.0002279209,0.0004720953,0.006654105,0.0002200696,0.0005753573,0.0008286545,0.0004185109,0.0006267949],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.003287667,"about_ca_system_score_gemma":0.005673288,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.3272071,"about_ca_topic_score_gemma":0.4362805,"domain_scores_codex":[0.9939139,0.00117299,0.001363027,0.0009684531,0.002111756,0.0004698623],"domain_scores_gemma":[0.9852231,0.001994876,0.00550956,0.001873922,0.004800142,0.0005984824],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001340477,0.0000287904,0.9746953,0.0003471661,0.0002292983,0.00007472805,0.0002107543,0.0007885685,0.0003037479,0.0002423846,0.01186824,0.0110769],"study_design_scores_gemma":[0.00002149587,0.00003624141,0.9869173,0.0001890865,0.00005616022,0.0001952894,0.0002752499,0.0008557305,0.0002163053,0.0001175036,0.01109389,0.00002568225],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"dataset","genre_gemma":"empirical","genre_scores_codex":[0.4730936,0.002064962,0.004244573,0.001098766,0.00004057104,0.000592454,0.5131005,0.0002461006,0.005518473],"genre_scores_gemma":[0.6400989,0.000950798,0.00795718,0.0003889636,0.00003468517,0.0008677952,0.3488499,0.00004128128,0.0008104338],"genre_candidate":"empirical","genre_consensus":null,"teacher_disagreement_score":0.3272071,"threshold_uncertainty_score":0.6506051,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03118785973395963,"score_gpt":0.2847769805860794,"score_spread":0.2535891208521197,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}