{"id":"W4385797947","doi":"10.1017/cjn.2023.274","title":"Infant with Macrocephaly, Refractory Seizures, and a Leukodystrophy","year":2023,"lang":"en","type":"article","venue":"Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques","topic":"Alcoholism and Thiamine Deficiency","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of Toronto","funders":"","keywords":"Macrocephaly; Leukodystrophy; Medicine; Refractory (planetary science); Pediatrics; Internal medicine; Biology; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["sts"],"consensus_categories":["sts"],"category_scores_codex":[0.002632769,0.0003150983,0.000567022,0.001353276,0.002095414,0.0004553149,0.0008481045,0.0001669005,0.0001170348],"category_scores_gemma":[0.001285209,0.0001791122,0.0001447099,0.002125444,0.007186727,0.0007228584,0.00006772813,0.001195337,0.000008348391],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001176575,"about_ca_system_score_gemma":0.003304668,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001029775,"about_ca_topic_score_gemma":0.009826059,"domain_scores_codex":[0.9963449,0.0003542413,0.0006365852,0.0005096906,0.0008640066,0.001290597],"domain_scores_gemma":[0.9964652,0.0003837901,0.0004914819,0.0001460299,0.000362926,0.002150542],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003555903,0.0000327616,0.9396353,0.00002750007,0.0000293384,0.05106451,0.0005723408,0.0004750586,0.000163789,0.001023852,0.002518791,0.004101214],"study_design_scores_gemma":[0.001291397,0.1862803,0.533307,0.0001292225,0.0001505597,0.2553734,0.0005342648,0.001540518,0.00009780476,0.003345253,0.01744743,0.000502881],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9899383,0.001129122,0.00000910788,0.004723458,0.000378735,0.0001512075,0.000009176461,0.00003575351,0.003625155],"genre_scores_gemma":[0.996165,0.0006972036,0.0007012392,0.002079799,0.000241869,0.000002170703,5.260147e-7,0.00001380902,0.00009832748],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.4063283,"threshold_uncertainty_score":0.9992037,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02984167046779715,"score_gpt":0.2730958088071538,"score_spread":0.2432541383393567,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}