{"id":"W4385797947","doi":"10.1017/cjn.2023.274","title":"Infant with Macrocephaly, Refractory Seizures, and a Leukodystrophy","year":2023,"lang":"en","type":"article","venue":"Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques","topic":"Alcoholism and Thiamine Deficiency","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of Toronto","funders":"","keywords":"Macrocephaly; Leukodystrophy; Medicine; Refractory (planetary science); Pediatrics; Internal medicine; Biology; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002236048,0.001074329,0.000665054,0.002030954,0.001102976,0.0005245773,0.0005653613,0.00207493,0.002984067],"category_scores_gemma":[0.002053277,0.0005022975,0.0004681852,0.0008657826,0.0007715388,0.0006379131,0.0005950261,0.002509519,0.0006136287],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0009595055,"about_ca_system_score_gemma":0.0008281766,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.01076159,"about_ca_topic_score_gemma":0.01596411,"domain_scores_codex":[0.9997118,0.00003809357,0.00002940523,0.00004322318,0.0000843382,0.00009303117],"domain_scores_gemma":[0.9994155,0.0001887062,0.0000841523,0.00002497083,0.00004965559,0.0002370414],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.00005200876,0.00003368963,0.003839949,0.00002759571,0.000007037191,0.9919798,0.000147881,0.00006723236,0.0007813291,0.0003997356,0.0007736133,0.001890207],"study_design_scores_gemma":[0.00001872333,0.0001631034,0.02923654,0.00006931437,0.00001914383,0.967945,0.0001432881,0.0002140619,0.0004182353,0.0004950315,0.001257711,0.00001981558],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9326803,0.004363788,0.00303194,0.01214562,0.0009270751,0.0002396761,0.001909008,0.0003861855,0.04431649],"genre_scores_gemma":[0.9876304,0.002460963,0.001104941,0.001860245,0.0003561705,0.0000347009,0.0002983492,0.00004156023,0.006212618],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01076159,"threshold_uncertainty_score":0.02139789,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02984167046779715,"score_gpt":0.2730958088071538,"score_spread":0.2432541383393567,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}