{"id":"W4386122831","doi":"10.1097/01.hs9.0000977204.63685.a6","title":"PB2629: LATE DIAGNOSIS OF TWO ADULT SIBLINGS WITH BERNARD SOULIER SYNDROME (BSS)","year":2023,"lang":"en","type":"article","venue":"HemaSphere","topic":"Platelet Disorders and Treatments","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"McMaster University","funders":"","keywords":"Bernard–Soulier syndrome; Medicine; Tranexamic acid; Ristocetin; Von Willebrand disease; Platelet; Von Willebrand factor; Vaginal bleeding; Coagulation; Pediatrics; Desmopressin; Platelet disorder; Bleeding time; Severe bleeding; Surgery; Internal medicine; Pregnancy; Platelet aggregation; Blood loss","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00004233965,0.0001819376,0.0004379765,0.00007344325,0.0000436535,0.000009792974,0.00006900362,0.00007416309,0.0006933953],"category_scores_gemma":[0.00003123581,0.0001325269,0.000100545,0.0005814098,0.00005908061,0.00007016046,0.00003659662,0.0001176152,0.0005675878],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002534268,"about_ca_system_score_gemma":0.00004918402,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0002736882,"about_ca_topic_score_gemma":0.0001233517,"domain_scores_codex":[0.9989024,0.00001186766,0.0002084679,0.0002662774,0.0003038338,0.0003071156],"domain_scores_gemma":[0.9993343,0.0000598709,0.00008748923,0.0002812123,0.0001022269,0.0001348906],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003571216,0.0007257833,0.9656429,0.0005215852,0.0009437047,0.01056357,0.000703839,0.00009114797,0.0006285048,0.0003523195,0.0126951,0.006774389],"study_design_scores_gemma":[0.07077443,0.009211089,0.804799,0.00738488,0.003755954,0.004854851,0.003857576,0.002704985,0.05389501,0.006955173,0.02920123,0.002605874],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9922835,0.0002826176,0.000007932244,0.001078283,0.00005131633,0.0003169984,0.00002693927,0.0001436165,0.005808827],"genre_scores_gemma":[0.9933975,0.0004572527,0.0005937488,0.0002582154,0.00002166527,0.00008500052,0.00006196884,0.00004659466,0.005078103],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.160844,"threshold_uncertainty_score":0.7592192,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01335614780480649,"score_gpt":0.2661488682950382,"score_spread":0.2527927204902317,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}