{"id":"W4386587276","doi":"10.7759/cureus.44988","title":"Congenital Thrombotic Thrombocytopenic Purpura: A Rare Cause of Recurrent Thrombocytopenia and Anemia","year":2023,"lang":"en","type":"article","venue":"Cureus","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":2,"is_retracted":false,"has_abstract":true,"ca_institutions":"Pediatric Oncology Group","funders":"","keywords":"Medicine; ADAMTS13; Thrombotic thrombocytopenic purpura; Microangiopathic hemolytic anemia; Fresh frozen plasma; Asymptomatic; Rare disease; Pediatrics; Internal medicine; Disease; Gastroenterology; Platelet","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001157646,0.0008291324,0.0004522902,0.000743925,0.0005177233,0.0004406309,0.000434299,0.001664412,0.00273572],"category_scores_gemma":[0.001159705,0.0002273572,0.0002169199,0.0007154809,0.0005777577,0.0003475035,0.0004356478,0.0006813334,0.0005258447],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002358971,"about_ca_system_score_gemma":0.0002921765,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0007816137,"about_ca_topic_score_gemma":0.0008267963,"domain_scores_codex":[0.9997479,0.00003328822,0.00002634852,0.00006783236,0.00005452116,0.00007011132],"domain_scores_gemma":[0.9992093,0.0001920875,0.0003285044,0.00005724775,0.00004707818,0.0001658218],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.00008243995,0.00003751366,0.05642386,0.0002454096,0.00004529178,0.9129094,0.0002094532,0.0001000464,0.007495849,0.0008798544,0.002383763,0.01918705],"study_design_scores_gemma":[0.000004996578,0.0000260158,0.01181102,0.00001630614,0.00001322129,0.9860744,0.00003394252,0.000066649,0.0005653706,0.00006377603,0.001320591,0.000003690807],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9565192,0.0221427,0.005717846,0.001102242,0.000192961,0.00007016808,0.000533092,0.0005386675,0.01318326],"genre_scores_gemma":[0.9947367,0.002654172,0.000983082,0.00017603,0.000231429,0.0000116699,0.0001957691,0.00003101025,0.0009801196],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.00273572,"threshold_uncertainty_score":0.009151936,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04490672299740075,"score_gpt":0.2996497169224938,"score_spread":0.2547429939250931,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}