{"id":"W4387840713","doi":"10.1111/pde.15459","title":"Characteristics and onset of presentation of pediatric stiff skin syndrome: A retrospective cohort study of 11 patients in a tertiary care center","year":2023,"lang":"en","type":"article","venue":"Pediatric Dermatology","topic":"Skin Diseases and Diabetes","field":"Medicine","cited_by":6,"is_retracted":false,"has_abstract":true,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of Toronto","funders":"","keywords":"Medicine; Magnetic resonance imaging; Radiology; Cohort; Retrospective cohort study; Ultrasound; SSS*; Interquartile range; Pelvic girdle; Surgery; Pathology; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00006563056,0.0001237384,0.0005707217,0.0006184567,0.00001482351,0.000002269179,0.00006659124,0.00008449472,0.00001703531],"category_scores_gemma":[0.0003022728,0.0001173917,0.00005297592,0.0006342062,0.00004564204,0.00004583381,0.00009375178,0.00008121425,0.000002399898],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002698557,"about_ca_system_score_gemma":0.00006199072,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0001903219,"about_ca_topic_score_gemma":0.00002701561,"domain_scores_codex":[0.9986087,0.00009659216,0.0005938947,0.000236723,0.0002717042,0.000192407],"domain_scores_gemma":[0.9990103,0.0001718854,0.0003257797,0.0001980275,0.0002238003,0.00007020166],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00007953738,0.001033869,0.9960459,0.0009739642,0.00002995884,0.00009407051,0.001301047,6.870686e-7,0.000001341268,0.000001716204,0.0003843021,0.00005353573],"study_design_scores_gemma":[0.003102832,0.000291765,0.9951358,0.00001420349,0.0004663509,0.00002414218,0.0008215341,0.0000312289,0.00002123353,0.00001335023,6.52047e-7,0.00007689808],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9983917,0.0002318049,5.014473e-7,0.00001630762,0.0001310633,0.0009109664,0.0002808066,0.00001688639,0.00001996029],"genre_scores_gemma":[0.9992225,0.000381059,0.00001184814,0.00001101566,0.00003445662,0.00005043164,0.0002700184,0.0000150766,0.000003579711],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003023295,"threshold_uncertainty_score":0.4787093,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.005787749102139177,"score_gpt":0.257064843719753,"score_spread":0.2512770946176138,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}