{"id":"W4389233640","doi":"10.1182/blood-2023-190722","title":"Cellular and Molecular Analysis of Hematopoietic Stem and Progenitor Cells in Shwachman-Diamond Syndrome","year":2023,"lang":"en","type":"article","venue":"Blood","topic":"Blood disorders and treatments","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Princess Margaret Cancer Centre; Children's Hospital of Eastern Ontario; University Health Network; SickKids Foundation; University of Toronto; Centre Hospitalier Universitaire Sainte-Justine; Hospital for Sick Children","funders":"","keywords":"Progenitor cell; Stem cell; Haematopoiesis; Biology; Myeloid; CD34; Bone marrow; Bone marrow failure; Immunology; Cancer research; Cell biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001931632,0.0002453905,0.0001941443,0.001221341,0.0002438847,0.0002006574,0.0002054006,0.0003313551,0.0007144521],"category_scores_gemma":[0.0003187289,0.0001267948,0.0001496972,0.0005446982,0.0003604426,0.0001365207,0.0002957481,0.0002731669,0.0001313176],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001916545,"about_ca_system_score_gemma":0.0001100256,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001127422,"about_ca_topic_score_gemma":0.001042014,"domain_scores_codex":[0.9998071,0.00002626999,0.00002411192,0.00004644384,0.0000725946,0.00002353933],"domain_scores_gemma":[0.999884,0.00003206487,0.0000249934,0.00001047251,0.00001798107,0.00003039306],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0005124653,0.00007101484,0.1582451,0.0001014229,0.00005173989,0.002630336,0.0006253417,0.0003502796,0.8219457,0.0003146828,0.0001051084,0.01504683],"study_design_scores_gemma":[0.00004495148,0.00089502,0.8180706,0.0000191307,0.00009569102,0.01608742,0.0007682133,0.001952893,0.1598897,0.0004803383,0.001673822,0.00002223851],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9989649,0.00031316,0.0004530545,0.000008621791,0.00000187949,0.000008437141,0.00009122833,0.000007111807,0.0001514313],"genre_scores_gemma":[0.9986346,0.0002025838,0.0008776304,0.00001976019,0.000002971961,0.00001478765,0.0001347183,0.000003070995,0.0001098],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001221341,"threshold_uncertainty_score":0.002390087,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.005587320670356334,"score_gpt":0.2096723574748098,"score_spread":0.2040850368044535,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}