{"id":"W4389617978","doi":"10.1053/j.akdh.2023.06.002","title":"Assessing the Risk of Progression to Kidney Failure in Patients With Autosomal Dominant Polycystic Kidney Disease","year":2023,"lang":"en","type":"article","venue":"Advances in Kidney Disease and Health","topic":"Genetic and Kidney Cyst Diseases","field":"Biochemistry, Genetics and Molecular Biology","cited_by":8,"is_retracted":false,"has_abstract":false,"ca_institutions":"Toronto General Hospital; University of Toronto; University Health Network; St. Joseph’s Healthcare Hamilton; McMaster University; Population Health Research Institute","funders":"Kidney Foundation of Canada; Canadian Institutes of Health Research; Canadian Society of Nephrology","keywords":"Autosomal dominant polycystic kidney disease; Medicine; PKD1; Family history; Genetic testing; Renal function; Polycystic kidney disease; Disease; Kidney disease; Intensive care medicine; Risk assessment; Genetic counseling; Risk stratification; Internal medicine; Pediatrics; Biology; Genetics","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001150129,0.0005499678,0.0007361436,0.001076942,0.0007668761,0.001169551,0.0005317815,0.001045206,0.0008315924],"category_scores_gemma":[0.004018758,0.0002956497,0.0008375698,0.00100195,0.0003638854,0.0007527001,0.0007536433,0.001565731,0.0002393959],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000349009,"about_ca_system_score_gemma":0.0004976779,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002914458,"about_ca_topic_score_gemma":0.00354211,"domain_scores_codex":[0.9992695,0.000276393,0.00009037423,0.000122327,0.0001541028,0.00008717361],"domain_scores_gemma":[0.9976959,0.0006122206,0.0008259912,0.0001334479,0.0002285482,0.000503848],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001436365,0.00002809821,0.9987193,0.000004558604,0.00003016519,0.00009091099,0.0000196867,0.00005342405,0.0000897841,0.00001086109,0.00002866196,0.000780954],"study_design_scores_gemma":[0.000008179202,0.0002952369,0.9973266,0.000007926579,0.00006551051,0.001034134,0.0001381936,0.0007460122,0.0001323691,0.0001025838,0.000133017,0.00001025702],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9979899,0.0004100025,0.0002211206,0.000102878,0.00001387766,0.00001075283,0.0002243334,0.00001277895,0.001014374],"genre_scores_gemma":[0.9990934,0.0001611386,0.0002273725,0.00004239098,0.0000161502,0.000006161228,0.000226802,0.000002899036,0.0002236229],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002914458,"threshold_uncertainty_score":0.006082535,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.007148386978463617,"score_gpt":0.3087879703366039,"score_spread":0.3016395833581403,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}