{"id":"W4390122614","doi":"10.1212/nxi.0000000000200191","title":"CNS Inflammation as the First Sign of Complement Factor I Deficiency","year":2023,"lang":"en","type":"article","venue":"Neurology Neuroimmunology & Neuroinflammation","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":15,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre Hospitalier Universitaire Sainte-Justine","funders":"Alexion Pharmaceuticals; Sanofi","keywords":"Medicine; Complement deficiency; Eculizumab; Inflammation; Immunology; Blockade; Complement system; Complement component 5; Internal medicine; Antibody; Receptor","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000200737,0.0007743008,0.0005388414,0.0007648898,0.0006149096,0.0005183094,0.0004183566,0.001174343,0.00254382],"category_scores_gemma":[0.001150152,0.0002714578,0.0002440263,0.0004026076,0.0008230637,0.0006800286,0.0005155868,0.001265593,0.0005722828],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006195643,"about_ca_system_score_gemma":0.0006206905,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001571216,"about_ca_topic_score_gemma":0.001626372,"domain_scores_codex":[0.9997873,0.00003205596,0.00002090203,0.00004457092,0.000041396,0.00007389522],"domain_scores_gemma":[0.9995201,0.0001250737,0.0001501438,0.00003583525,0.00005931093,0.0001095414],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.000243131,0.00005166373,0.03493636,0.0002092904,0.00002216804,0.9462149,0.0002601489,0.0001155599,0.009699745,0.00050106,0.001052973,0.006693073],"study_design_scores_gemma":[0.00002256117,0.0001717659,0.02347757,0.00009304995,0.00002429817,0.9710516,0.0001688349,0.0002808596,0.002852728,0.0003207046,0.001523775,0.00001228076],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.957845,0.01417784,0.003633011,0.001677827,0.0002468516,0.0002132402,0.0003520233,0.0002525335,0.02160169],"genre_scores_gemma":[0.9958689,0.001986264,0.0009591577,0.0002516463,0.0001362426,0.00001440813,0.00007584035,0.000007796952,0.0006996649],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.00254382,"threshold_uncertainty_score":0.008509874,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02458383152584899,"score_gpt":0.2565551249789961,"score_spread":0.2319712934531472,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}