{"id":"W4390144815","doi":"10.1002/mds.29687","title":"Predictors of Survival in Friedreich's Ataxia: A Prospective Cohort Study","year":2023,"lang":"en","type":"article","venue":"Movement Disorders","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":26,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University","funders":"European Commission","keywords":"Medicine; Hazard ratio; Internal medicine; Proportional hazards model; Prospective cohort study; Survival analysis; Log-rank test; Cohort; Ataxia; Confidence interval; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002303677,0.0001813126,0.000246257,0.000220063,0.00006840337,0.00001874562,0.0002761689,0.00002399641,0.00007237395],"category_scores_gemma":[0.0004221475,0.0001777476,0.0000599678,0.001071522,0.0001148365,0.00007535215,0.000179642,0.00009353997,0.00003728136],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00004937764,"about_ca_system_score_gemma":0.00004870761,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0001961429,"about_ca_topic_score_gemma":0.000737912,"domain_scores_codex":[0.9978624,0.0002374039,0.0003190745,0.0006171266,0.0006330647,0.0003309157],"domain_scores_gemma":[0.9993384,0.0001247943,0.00009005539,0.0003540649,0.00002857817,0.00006404213],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00003665261,0.0008351064,0.9719155,0.00001074115,0.00001741246,0.000009095669,0.0007774237,0.001121486,0.02447462,0.0002432821,0.0005021238,0.00005657524],"study_design_scores_gemma":[0.0009544312,0.0003016537,0.9275371,0.000005243385,0.00001500156,9.797037e-9,0.001542471,0.0001828394,0.0668432,0.002456954,0.00002093056,0.0001401136],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9950091,0.000009987405,0.00001695294,0.0001522343,0.0003505586,0.002146889,0.00005931329,0.00009889991,0.00215602],"genre_scores_gemma":[0.9987776,0.00003793604,0.0000035319,0.0002322081,0.00001568801,0.0004419703,0.000006186125,0.0000264214,0.0004584927],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.04437833,"threshold_uncertainty_score":0.7248337,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0172749863199159,"score_gpt":0.2659396897626806,"score_spread":0.2486647034427647,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}