{"id":"W4390144815","doi":"10.1002/mds.29687","title":"Predictors of Survival in Friedreich's Ataxia: A Prospective Cohort Study","year":2023,"lang":"en","type":"article","venue":"Movement Disorders","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":26,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University","funders":"European Commission","keywords":"Medicine; Hazard ratio; Internal medicine; Proportional hazards model; Prospective cohort study; Survival analysis; Log-rank test; Cohort; Ataxia; Confidence interval; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.002042354,0.0004286264,0.0004940081,0.0009050865,0.0005877799,0.0008229782,0.0004525576,0.000621339,0.001167888],"category_scores_gemma":[0.003147379,0.0003556686,0.0008019406,0.001177078,0.0003227699,0.0007796832,0.000616133,0.001047591,0.0002524639],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003093359,"about_ca_system_score_gemma":0.0005065307,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.004081627,"about_ca_topic_score_gemma":0.004170036,"domain_scores_codex":[0.9993132,0.000192479,0.00007067354,0.0001944829,0.00009626224,0.0001329616],"domain_scores_gemma":[0.9978592,0.0004873295,0.0007157448,0.0002987324,0.0002449187,0.0003940388],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001908582,0.00003602758,0.998969,0.000003637751,0.00006503383,0.00006050033,0.00003377456,0.00004384404,0.00005536082,0.00001007621,0.00006803688,0.0004639033],"study_design_scores_gemma":[0.00002917688,0.0002930906,0.9985496,0.000008653422,0.0001050643,0.0002660184,0.0001133531,0.0004085306,0.00003053861,0.00004129235,0.0001475874,0.000007126731],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9992188,0.0001479685,0.00008797184,0.00002778718,0.00000474232,0.00001052428,0.0003873763,0.000002976509,0.0001117116],"genre_scores_gemma":[0.9991571,0.0001076304,0.00008398657,0.00001753845,0.000009391264,0.0000138133,0.0005314441,0.000002371729,0.00007669544],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.004081627,"threshold_uncertainty_score":0.01080114,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0172749863199159,"score_gpt":0.2659396897626806,"score_spread":0.2486647034427647,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}