{"id":"W4390262166","doi":"10.1016/j.jns.2023.121003","title":"Friedreich ataxia","year":2023,"lang":"de","type":"article","venue":"Journal of the Neurological Sciences","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"McGill University","funders":"","keywords":"Ataxia; Medicine; Physical medicine and rehabilitation; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002097109,0.001024361,0.0005479165,0.001219889,0.001316824,0.0008782136,0.000439749,0.0008408144,0.02592411],"category_scores_gemma":[0.0005447673,0.0001500314,0.0003756389,0.0008728777,0.0003553614,0.0004721156,0.0006259015,0.0005933433,0.01178974],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006451815,"about_ca_system_score_gemma":0.0007428242,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.006075933,"about_ca_topic_score_gemma":0.004796767,"domain_scores_codex":[0.9998428,0.00001601453,0.00001773733,0.00005226427,0.00003724911,0.00003386208],"domain_scores_gemma":[0.9998326,0.00001993014,0.00003078677,0.00001865326,0.00005053228,0.00004743575],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.002065313,0.0009425898,0.0981614,0.0007285879,0.0005189755,0.1377693,0.001098108,0.0007538048,0.1306889,0.03344573,0.1456605,0.4481668],"study_design_scores_gemma":[0.0002511133,0.0007533076,0.1675207,0.0003869899,0.0004703276,0.2706529,0.0004521402,0.001015374,0.03211842,0.01215244,0.5141254,0.0001009404],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"other","genre_scores_codex":[0.5097958,0.02436757,0.01546289,0.004478002,0.001448876,0.00068008,0.01670471,0.003392099,0.42367],"genre_scores_gemma":[0.7325639,0.006508415,0.005735118,0.001691736,0.0002655579,0.0001421384,0.01402118,0.0001554859,0.2389165],"genre_candidate":"other","genre_consensus":null,"teacher_disagreement_score":0.02592411,"threshold_uncertainty_score":0.08672482,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.07402470554184125,"score_gpt":0.3127407413839172,"score_spread":0.2387160358420759,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}