{"id":"W4390350774","doi":"10.1016/j.cell.2023.11.036","title":"Human inherited CCR2 deficiency underlies progressive polycystic lung disease","year":2023,"lang":"en","type":"article","venue":"Cell","topic":"Neonatal Respiratory Health Research","field":"Medicine","cited_by":53,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University","funders":"H2020 European Research Council; National Center for Advancing Translational Sciences; National Cancer Institute; National Heart, Lung, and Blood Institute; Instituto Nacional del Cáncer; National Institutes of Health; Canadian Institutes of Health Research; Université de Paris; Honjo International Scholarship Foundation; Agence Nationale de Recherches sur le Sida et les Hépatites Virales; Assistance Publique - Hôpitaux de Paris; Division of Agriculture and Natural Resources, University of California; Université de Strasbourg; Institut National de la Santé et de la Recherche Médicale; Institut des maladies génétiques Imagine; Deutsche Forschungsgemeinschaft; Vaccine Research Center; Texas Biomedical Research Institute; Fondation pour la Recherche Médicale; Rockefeller University; European Molecular Biology Organization; St. Giles Foundation; American Thoracic Society; Centre National de la Recherche Scientifique; Fondation Bettencourt Schueller; National Institute of Allergy and Infectious Diseases; Agence Nationale de la Recherche; Howard Hughes Medical Institute","keywords":"Biology; Disease; Lung; Lung disease; Genetics; Internal medicine","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001604364,0.0008139539,0.0003412534,0.0002835612,0.0003652056,0.0002086705,0.0001817684,0.0003722297,0.001808548],"category_scores_gemma":[0.0004429234,0.0001152611,0.0001618647,0.0002082193,0.000470309,0.0001274755,0.0003320878,0.0003211547,0.0002794208],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001514128,"about_ca_system_score_gemma":0.000183865,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000994821,"about_ca_topic_score_gemma":0.001073219,"domain_scores_codex":[0.9998397,0.00003220991,0.00001671303,0.00005202079,0.00003321602,0.0000261362],"domain_scores_gemma":[0.9998119,0.00004390586,0.00004929524,0.00001503442,0.0000191889,0.0000606047],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.00146659,0.000212891,0.1102568,0.000557051,0.0003383411,0.2837045,0.0012,0.0010132,0.5433311,0.002933692,0.004742013,0.05024371],"study_design_scores_gemma":[0.0001661693,0.0008384755,0.212785,0.0001032204,0.0003555201,0.7295297,0.0003434929,0.001284712,0.03841366,0.0008190967,0.01530285,0.00005813904],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.991064,0.002919795,0.003120795,0.000234156,0.00005201667,0.00003216096,0.000464347,0.00008208391,0.00203065],"genre_scores_gemma":[0.9973509,0.0006885245,0.0009619978,0.00008581187,0.00003508183,0.000009257011,0.0002486733,0.00001169247,0.0006080413],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001808548,"threshold_uncertainty_score":0.006050229,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05842371463733139,"score_gpt":0.3934821905651001,"score_spread":0.3350584759277687,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}