{"id":"W4391499865","doi":"10.1016/j.jacadv.2024.100832","title":"Long-Term Arrhythmic Follow-Up and Risk Stratification of Patients With Desmoplakin-Associated Arrhythmogenic Right Ventricular Cardiomyopathy","year":2024,"lang":"en","type":"article","venue":"JACC Advances","topic":"Cardiovascular Effects of Exercise","field":"Medicine","cited_by":41,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Montréal; Montreal Heart Institute","funders":"Ministero dell'Istruzione e del Merito; Netherlands Heart Institute; Medical Research Council; Biosense Webster; National Institutes of Health; Rosetrees Trust; Bayer HealthCare; Hartstichting; Imperial College London; Daiichi-Sankyo; National Institute for Health and Care Research; Cytokinetics; British Heart Foundation; National Center for Advancing Translational Sciences; Wellcome Trust; Johns Hopkins University; National Heart, Lung, and Blood Institute; Pfizer; Bristol-Myers Squibb; Boston Scientific Corporation; Sarepta Therapeutics; Rose Foundation for Communities and the Environment","keywords":"Desmoplakin; Risk stratification; Medicine; Cardiology; Internal medicine; Cardiomyopathy; Term (time); Heart failure; Physics; Genetics; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0008815373,0.0002100589,0.0002705196,0.0005641599,0.0003228416,0.0005703956,0.0002645406,0.0003658245,0.000444477],"category_scores_gemma":[0.003368712,0.0001264296,0.0002877564,0.000514685,0.0001899467,0.0005077861,0.0003860581,0.0003776246,0.0001540979],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001996598,"about_ca_system_score_gemma":0.0001751617,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009553445,"about_ca_topic_score_gemma":0.001351073,"domain_scores_codex":[0.9995927,0.0001210383,0.00005616411,0.00009362261,0.00008023767,0.00005633411],"domain_scores_gemma":[0.9982986,0.0003930728,0.0007247902,0.0001293228,0.0001777034,0.0002766519],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00008154998,0.00001776307,0.9985304,0.00000172508,0.0000152681,0.00005332995,0.00002157748,0.00003604372,0.00007239971,0.000006266064,0.00002404207,0.001139613],"study_design_scores_gemma":[0.000007532024,0.0001237734,0.9989572,0.000003594299,0.00002392992,0.0002395825,0.00007713424,0.0004172788,0.00005572964,0.00002753006,0.00006374597,0.000003052537],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9996172,0.0001091261,0.00005602719,0.00001920548,0.000002940639,0.000002459155,0.0000631935,0.00000153333,0.0001283225],"genre_scores_gemma":[0.9996598,0.00004764529,0.00004952597,0.00001311941,0.000009659163,0.00000257568,0.0001786616,5.637878e-7,0.0000384401],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0009553445,"threshold_uncertainty_score":0.004662097,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.003658085908949465,"score_gpt":0.2252230869906009,"score_spread":0.2215650010816514,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}