{"id":"W4391499865","doi":"10.1016/j.jacadv.2024.100832","title":"Long-Term Arrhythmic Follow-Up and Risk Stratification of Patients With Desmoplakin-Associated Arrhythmogenic Right Ventricular Cardiomyopathy","year":2024,"lang":"en","type":"article","venue":"JACC Advances","topic":"Cardiovascular Effects of Exercise","field":"Medicine","cited_by":41,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Montréal; Montreal Heart Institute","funders":"Ministero dell'Istruzione e del Merito; Netherlands Heart Institute; Medical Research Council; Biosense Webster; National Institutes of Health; Rosetrees Trust; Bayer HealthCare; Hartstichting; Imperial College London; Daiichi-Sankyo; National Institute for Health and Care Research; Cytokinetics; British Heart Foundation; National Center for Advancing Translational Sciences; Wellcome Trust; Johns Hopkins University; National Heart, Lung, and Blood Institute; Pfizer; Bristol-Myers Squibb; Boston Scientific Corporation; Sarepta Therapeutics; Rose Foundation for Communities and the Environment","keywords":"Desmoplakin; Risk stratification; Medicine; Cardiology; Internal medicine; Cardiomyopathy; Term (time); Heart failure; Physics; Genetics; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003167735,0.000244964,0.0005878002,0.0001839771,0.00007866593,0.00004160231,0.00006148391,0.0001038842,0.00002649839],"category_scores_gemma":[0.0001559457,0.0001838319,0.0003016408,0.0004480459,0.0001078534,0.0003205244,0.00002956633,0.000210407,0.00001284807],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000110394,"about_ca_system_score_gemma":0.00007767515,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00001571577,"about_ca_topic_score_gemma":0.00003310944,"domain_scores_codex":[0.9983193,0.0001038899,0.0003154051,0.0004789631,0.0005277349,0.0002547588],"domain_scores_gemma":[0.9989516,0.0001322163,0.0001703663,0.0004289317,0.0002006044,0.0001163367],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0007472975,0.0001542319,0.9059937,0.0008905508,0.001784903,0.001263803,0.000174442,0.000113695,0.0002686197,0.00003369388,0.00007442819,0.08850062],"study_design_scores_gemma":[0.003584658,0.0004789293,0.987454,0.0008841166,0.002217229,0.0001617238,0.00002333521,0.0001534663,0.003777537,0.0001510918,0.0008204403,0.0002934665],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.967434,0.02967375,0.001165916,0.00002077034,0.0003867622,0.0009961708,0.00008366428,0.0001048069,0.0001341711],"genre_scores_gemma":[0.997429,0.001621201,0.0003865662,0.000006740454,0.000134557,0.00009756772,0.0001934033,0.00004256366,0.00008844485],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.08820715,"threshold_uncertainty_score":0.7496448,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.003658085908949465,"score_gpt":0.2252230869906009,"score_spread":0.2215650010816514,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}