{"id":"W4391606017","doi":"10.1002/j.1536-4801.2006.tb13816.x","title":"HYPERORNITHINEMIA, HYPERAMMONEMIA, HOMOCITRULLINEMIA (HHH) SYNDROME PRESENTING WITH SEVERE LIVER FAILURE","year":2006,"lang":"en","type":"article","venue":"Journal of Pediatric Gastroenterology and Nutrition","topic":"Metabolism and Genetic Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Alberta Hospital","funders":"","keywords":"Hyperammonemia; Medicine; Liver failure; Pediatrics; Surgery; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001063337,0.001380208,0.0006945288,0.001074622,0.0009177449,0.0003897671,0.0003256435,0.001067894,0.001879604],"category_scores_gemma":[0.0009082275,0.000459513,0.0003489324,0.001027135,0.0006847571,0.0007082314,0.0006130695,0.001012874,0.0004014676],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003286852,"about_ca_system_score_gemma":0.0003889246,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002378979,"about_ca_topic_score_gemma":0.003516407,"domain_scores_codex":[0.9998091,0.000023297,0.00002286023,0.00004743857,0.00003797765,0.00005930081],"domain_scores_gemma":[0.9996961,0.00006703798,0.0000844122,0.00001197513,0.00002350818,0.0001170111],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.00006604208,0.00003416713,0.0245603,0.00008981011,0.00001417197,0.967594,0.0001802582,0.00007975895,0.004310417,0.0001107117,0.0003524837,0.002607986],"study_design_scores_gemma":[0.00001370395,0.0001142238,0.03244927,0.00001908198,0.00002057284,0.9654447,0.0001021839,0.0001252142,0.000895276,0.0001331184,0.0006728862,0.000009794362],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9798887,0.005291158,0.002425131,0.001102287,0.0001243078,0.0001724488,0.0003451317,0.0002185073,0.01043225],"genre_scores_gemma":[0.9952152,0.002039605,0.0006339161,0.0004979954,0.0001385686,0.00002439521,0.0001497355,0.00001852767,0.001282123],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002378979,"threshold_uncertainty_score":0.006287873,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.003315832261237796,"score_gpt":0.1831128230311529,"score_spread":0.1797969907699151,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}