{"id":"W4392055726","doi":"10.1016/j.jcf.2024.01.012","title":"ECFS standards of care on CFTR-related disorders: Towards a comprehensive program for affected individuals","year":2024,"lang":"en","type":"article","venue":"Journal of Cystic Fibrosis","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":16,"is_retracted":false,"has_abstract":false,"ca_institutions":"Hospital for Sick Children; University of Toronto","funders":"","keywords":"Cystic fibrosis; Cystic fibrosis transmembrane conductance regulator; Medicine; Health professionals; Newborn screening; Health care; Intensive care medicine; Bioinformatics; Pediatrics; Internal medicine; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.04864683,0.0009185913,0.001065924,0.004047176,0.003812889,0.004920224,0.004606834,0.01311075,0.01054177],"category_scores_gemma":[0.09229883,0.0006572016,0.002175968,0.001288234,0.002804832,0.004348763,0.01413625,0.01297384,0.00321585],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.009830641,"about_ca_system_score_gemma":0.1138726,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.03451645,"about_ca_topic_score_gemma":0.03399149,"domain_scores_codex":[0.9662322,0.01130073,0.004249875,0.001625679,0.01202074,0.004570846],"domain_scores_gemma":[0.8559511,0.01546287,0.007273228,0.007064109,0.05704199,0.05720665],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001653269,0.002005527,0.04096294,0.0006751365,0.0001038933,0.001374632,0.001919344,0.002887059,0.002531964,0.03489661,0.5837466,0.3287311],"study_design_scores_gemma":[0.0003567428,0.0008685985,0.1397602,0.007998147,0.0001483844,0.002870869,0.003231916,0.005422842,0.002617595,0.02648711,0.8099408,0.0002969222],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"commentary","genre_gemma":"other","genre_scores_codex":[0.02179821,0.006784178,0.04873075,0.8068619,0.01444358,0.002883767,0.001121418,0.002231776,0.09514432],"genre_scores_gemma":[0.2744979,0.01243142,0.1995904,0.3911243,0.0156374,0.006713377,0.006943513,0.001047582,0.092014],"genre_candidate":"other","genre_consensus":null,"teacher_disagreement_score":0.04864683,"threshold_uncertainty_score":0.2572721,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01232558212784632,"score_gpt":0.3560949670809218,"score_spread":0.3437693849530754,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}