{"id":"W4395063493","doi":"10.1016/j.clim.2024.109945","title":"3 Development of the Canadian Inborn Errors of Immunity National Registry (CIEINR)","year":2024,"lang":"en","type":"article","venue":"Clinical Immunology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":4,"is_retracted":false,"has_abstract":false,"ca_institutions":"Institute of Infection and Immunity; Western University; McMaster University; BC Children's Hospital; Calgary General Hospital; Montreal Clinical Research Institute; Izaak Walton Killam Health Centre; Alberta Children's Hospital; University of Ottawa; University of Alberta; Hospital for Sick Children; Alberta Health Services; University of Manitoba; Foothills Medical Centre; Dalhousie University; University of Calgary","funders":"","keywords":"Immunity; Medicine; Pediatrics; Immunology; Immune system","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.01194841,0.0006234751,0.0007485649,0.009187215,0.002409524,0.002998859,0.003085034,0.001390765,0.01240274],"category_scores_gemma":[0.02721085,0.0005362449,0.0009118489,0.005441125,0.0004307704,0.001199636,0.00235536,0.001639671,0.003217787],"about_ca_system_candidate":true,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.02264497,"about_ca_system_score_gemma":0.1455456,"about_ca_topic_candidate":true,"about_ca_topic_consensus":true,"about_ca_topic_score_codex":0.9083863,"about_ca_topic_score_gemma":0.9226982,"domain_scores_codex":[0.9919533,0.0008805756,0.0008744498,0.0005831923,0.004169858,0.001538607],"domain_scores_gemma":[0.9166154,0.004337355,0.004340277,0.002422302,0.06474843,0.007536091],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0003562995,0.0002088496,0.2157978,0.0005098599,0.0001380809,0.0006177326,0.0005456142,0.00152849,0.0008964104,0.01783136,0.6169521,0.1446175],"study_design_scores_gemma":[0.0001701683,0.00009160145,0.2480559,0.001073111,0.00009513569,0.0004129318,0.0007219181,0.002635444,0.001226822,0.001201399,0.7442006,0.0001149909],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"dataset","genre_gemma":"other","genre_scores_codex":[0.08333469,0.005670775,0.03677842,0.07182073,0.009634631,0.01253406,0.4919757,0.003209796,0.2850413],"genre_scores_gemma":[0.2633082,0.0085933,0.127918,0.02353614,0.002684181,0.005644873,0.4052408,0.001086096,0.1619885],"genre_candidate":"other","genre_consensus":null,"teacher_disagreement_score":0.977355,"threshold_uncertainty_score":0.1843063,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04466526199567474,"score_gpt":0.3269979823147363,"score_spread":0.2823327203190616,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}