{"id":"W4397024465","doi":"10.1681/asn.20223311s1189a","title":"Long-Term Outcomes in Eculizumab-Treated Patients Enrolled in the Global aHUS Registry","year":2022,"lang":"en","type":"article","venue":"Journal of the American Society of Nephrology","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children","funders":"","keywords":"Eculizumab; Atypical hemolytic uremic syndrome; Medicine; Term (time); Nephrology; Pediatrics; Internal medicine; Intensive care medicine; Immunology; Complement system; Antibody","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001928811,0.0001912753,0.0004740639,0.0007372382,0.0003608578,0.0009403075,0.0003649281,0.0003266515,0.0009023228],"category_scores_gemma":[0.004469937,0.0001441349,0.0004478073,0.001333038,0.0002563352,0.0007643477,0.0006902536,0.0006184484,0.0001845998],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004484624,"about_ca_system_score_gemma":0.000489282,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002213223,"about_ca_topic_score_gemma":0.00341427,"domain_scores_codex":[0.9988864,0.0003449352,0.0001885611,0.0002293333,0.000180749,0.0001699749],"domain_scores_gemma":[0.9961279,0.0005176828,0.002350932,0.0002736843,0.0002588,0.0004710675],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003725731,0.00005016441,0.9968415,0.00001332669,0.00009851047,0.000103041,0.00005368363,0.00007047642,0.00007425253,0.00003899259,0.0004853054,0.001798098],"study_design_scores_gemma":[0.00007496811,0.0003035977,0.9975805,0.00002967702,0.0001187381,0.0004605811,0.0002100801,0.0003371525,0.0001006434,0.00006162983,0.0007130051,0.000009266332],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9971514,0.0004064128,0.00007225699,0.0001150263,0.000009073015,0.0000151305,0.001646701,0.0000053831,0.0005786939],"genre_scores_gemma":[0.9956599,0.0002271714,0.00008941794,0.00009222171,0.00002064211,0.00003321128,0.00377709,0.000003773514,0.00009651516],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002213223,"threshold_uncertainty_score":0.01020062,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01553477521456575,"score_gpt":0.2818940998354691,"score_spread":0.2663593246209033,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}