{"id":"W4398255859","doi":"10.1017/cjn.2024.120","title":"P.012 A global, long-term, prospective, observational registry of patients with AQP4+ NMOSD treated with complement component 5 inhibitor therapies eculizumab or ravulizumab","year":2024,"lang":"en","type":"article","venue":"Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Eculizumab; Medicine; Observational study; Dosing; Population; Pediatrics; Adverse effect; Intensive care medicine; Internal medicine; Immunology; Immune system; Complement system","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["sts"],"consensus_categories":["sts"],"category_scores_codex":[0.001168729,0.000429076,0.0006516453,0.0005161892,0.001539492,0.000496889,0.001589498,0.0001409345,0.0007479612],"category_scores_gemma":[0.0003337329,0.0002277735,0.0001819285,0.001351842,0.006539257,0.0007692516,0.00007988003,0.0006516036,0.000004482486],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000457438,"about_ca_system_score_gemma":0.003804458,"about_ca_topic_candidate":true,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001038514,"about_ca_topic_score_gemma":0.04168082,"domain_scores_codex":[0.9958462,0.0008719533,0.001021864,0.0006304658,0.000562136,0.001067451],"domain_scores_gemma":[0.9971821,0.0004998115,0.0008487309,0.0002023886,0.0007375613,0.0005294583],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001090536,0.000122208,0.9933677,0.00003645567,0.0001483546,0.001812749,0.0001920771,0.000335694,0.00005402465,0.000873113,0.001126655,0.0008403789],"study_design_scores_gemma":[0.001143202,0.05355239,0.9363885,0.0002629193,0.0001021971,0.005838669,0.0001667514,0.00003420927,0.0001383753,0.0007198409,0.001356357,0.0002965682],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9944083,0.002797958,0.00004274975,0.001190701,0.0005077485,0.0004828779,0.0002353948,0.00003420065,0.0003000427],"genre_scores_gemma":[0.998921,0.00007039681,0.0004124774,0.0004492662,0.00008029103,0.00001121196,0.00001027515,0.00001342908,0.00003167444],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.05697924,"threshold_uncertainty_score":0.9997604,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03922132816123652,"score_gpt":0.2749463947731343,"score_spread":0.2357250666118977,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}