{"id":"W4399500634","doi":"10.1177/01455613241261563","title":"Short Cilia, Immunodeficiency, and Cystic Fibrosis in a Mother-Daughter Pair","year":2024,"lang":"en","type":"article","venue":"Ear Nose & Throat Journal","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Toronto; University of British Columbia","funders":"","keywords":"Primary ciliary dyskinesia; Refractory (planetary science); Cystic fibrosis; Medicine; Primary immunodeficiency; Immunodeficiency; Common variable immunodeficiency; Medical therapy; Daughter; Disease; Chronic rhinosinusitis; Pediatrics; Internal medicine; Immunology; Bronchiectasis; Lung; Biology; Immune system","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000721621,0.0001980728,0.0003363018,0.0003460671,0.0001188779,0.0002365635,0.0001365405,0.00008003442,0.0006397284],"category_scores_gemma":[0.0002924849,0.0001487315,0.0001216692,0.0004207181,0.0002009213,0.0003022134,0.00008786363,0.0008300696,0.0001165507],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002021968,"about_ca_system_score_gemma":0.0002038024,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00004413125,"about_ca_topic_score_gemma":0.00001786097,"domain_scores_codex":[0.998045,0.00009584847,0.0003960866,0.000321928,0.0006203499,0.0005207671],"domain_scores_gemma":[0.999188,0.0002407342,0.00002862933,0.00023515,0.00007282117,0.000234682],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.001847115,0.000808949,0.1157564,0.001432716,0.0004354535,0.008490139,0.007145802,0.000180991,0.4979122,0.0004587934,0.01411893,0.3514125],"study_design_scores_gemma":[0.003990395,0.003372513,0.8056067,0.00795742,0.0002875895,0.01973568,0.002400929,0.0147671,0.0112155,0.004559851,0.1250385,0.001067912],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9712712,0.02340706,0.00147228,0.001952982,0.0003549498,0.000278967,0.00001588734,0.00006856887,0.00117811],"genre_scores_gemma":[0.9943694,0.0008455399,0.003113417,0.0001030425,0.0002759201,0.000009978761,0.000003964764,0.00004308427,0.001235611],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.6898503,"threshold_uncertainty_score":0.7004577,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0155378636404472,"score_gpt":0.3142333966573371,"score_spread":0.2986955330168899,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}