{"id":"W4400687701","doi":"10.1007/s00401-024-02765-3","title":"Anti-Ku + myositis: an acquired inflammatory protein-aggregate myopathy","year":2024,"lang":"en","type":"article","venue":"Acta Neuropathologica","topic":"Inflammatory Myopathies and Dermatomyositis","field":"Medicine","cited_by":16,"is_retracted":false,"has_abstract":true,"ca_institutions":"Children's Hospital of Eastern Ontario","funders":"European Regional Development Fund; Universitätsklinikum Hamburg-Eppendorf; Deutsche Gesellschaft für Muskelkranke; Bundesministerium für Bildung und Forschung; Ministerium für Innovation, Wissenschaft und Forschung des Landes Nordrhein-Westfalen","keywords":"Myositis; Inclusion body myositis; Pathology; Polymyositis; Muscle biopsy; Dermatomyositis; Inflammatory myopathy; Myopathy; Inflammation; Biology; Medicine; Biopsy; Immunology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0005342523,0.0005330588,0.0006699807,0.0003216122,0.0003086197,0.00030278,0.0003483145,0.000308202,0.0003445274],"category_scores_gemma":[0.0001759854,0.0004322737,0.0002877853,0.0004656052,0.0003020703,0.0006918201,0.0002214759,0.0005404328,0.0007359486],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0000711422,"about_ca_system_score_gemma":0.0001920982,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000004374139,"about_ca_topic_score_gemma":9.507871e-7,"domain_scores_codex":[0.9965841,0.0003715194,0.0006857858,0.001025971,0.0005365117,0.000796116],"domain_scores_gemma":[0.998161,0.00007209371,0.0001403034,0.00103685,0.0001506658,0.0004390957],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.0002529919,0.0002297441,0.00432063,0.0006869095,0.00005224637,0.08086652,0.0009674702,0.000003932039,0.8961549,0.002195758,0.00286752,0.01140133],"study_design_scores_gemma":[0.003912752,0.005842421,0.395091,0.003249398,0.0007398407,0.05052784,0.0007041734,0.004238789,0.1953695,0.001657872,0.3355442,0.003122183],"study_design_candidate":"bench_or_experimental","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9874043,0.001312616,0.00007115856,0.001810167,0.0008221673,0.001052055,0.00003899709,0.001909246,0.005579283],"genre_scores_gemma":[0.9948615,0.0002525862,0.0005479019,0.002345805,0.0007677401,0.0001528053,0.00006332506,0.0001379216,0.0008703443],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.7007854,"threshold_uncertainty_score":0.9998129,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01358492271385292,"score_gpt":0.2555322759630874,"score_spread":0.2419473532492345,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}