{"id":"W4400687701","doi":"10.1007/s00401-024-02765-3","title":"Anti-Ku + myositis: an acquired inflammatory protein-aggregate myopathy","year":2024,"lang":"en","type":"article","venue":"Acta Neuropathologica","topic":"Inflammatory Myopathies and Dermatomyositis","field":"Medicine","cited_by":16,"is_retracted":false,"has_abstract":true,"ca_institutions":"Children's Hospital of Eastern Ontario","funders":"European Regional Development Fund; Universitätsklinikum Hamburg-Eppendorf; Deutsche Gesellschaft für Muskelkranke; Bundesministerium für Bildung und Forschung; Ministerium für Innovation, Wissenschaft und Forschung des Landes Nordrhein-Westfalen","keywords":"Myositis; Inclusion body myositis; Pathology; Polymyositis; Muscle biopsy; Dermatomyositis; Inflammatory myopathy; Myopathy; Inflammation; Biology; Medicine; Biopsy; Immunology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002483994,0.0006076206,0.0004519347,0.0006477429,0.0003604752,0.0003175324,0.000229154,0.0004100146,0.002236053],"category_scores_gemma":[0.0003868127,0.0001810518,0.000177872,0.0004823134,0.0005649237,0.0003099417,0.0004577542,0.0002113986,0.0004867672],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001740521,"about_ca_system_score_gemma":0.000127961,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0002845741,"about_ca_topic_score_gemma":0.0003213247,"domain_scores_codex":[0.9997666,0.00003727186,0.00003527287,0.00007979709,0.00004326119,0.00003775482],"domain_scores_gemma":[0.9997693,0.00002806901,0.0001140828,0.00001854279,0.00002602423,0.00004411652],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"case_report","study_design_scores_codex":[0.00235003,0.0003513193,0.6102361,0.001075488,0.0002116124,0.09784658,0.0007215578,0.0003578124,0.2537805,0.0006092544,0.0007404422,0.03171942],"study_design_scores_gemma":[0.0000581553,0.001306425,0.7443926,0.00003576699,0.00009614935,0.2417784,0.0002430166,0.0004079506,0.009482621,0.0001903514,0.001995622,0.00001283199],"study_design_candidate":"case_report","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9972329,0.001206214,0.0006074614,0.00003496652,0.000008039869,0.00001746074,0.00009862135,0.00002303067,0.0007713659],"genre_scores_gemma":[0.9990037,0.0002506269,0.0002790985,0.00003270377,0.00002731092,0.000005503419,0.00009450116,0.000004452887,0.000302112],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002236053,"threshold_uncertainty_score":0.007480323,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01358492271385292,"score_gpt":0.2555322759630874,"score_spread":0.2419473532492345,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}