{"id":"W4400702196","doi":"10.1701/4314.42986","title":"Sindrome del guardiano del faro: attualizzazione","year":2024,"lang":"en","type":"article","venue":"Recenti Progressi in Medicina","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Canadian Obesity Network","funders":"","keywords":"Medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000523131,0.001893531,0.001063146,0.002968286,0.002187423,0.001436396,0.0008212332,0.002876406,0.007356626],"category_scores_gemma":[0.002089832,0.0004213899,0.001038295,0.001578389,0.00226175,0.001463813,0.001420857,0.003886942,0.001959517],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001347365,"about_ca_system_score_gemma":0.0006594072,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.006024758,"about_ca_topic_score_gemma":0.00445117,"domain_scores_codex":[0.9994596,0.00008874924,0.00003722521,0.0001694674,0.00007672745,0.0001683723],"domain_scores_gemma":[0.9994425,0.0001665546,0.0001387298,0.0000904028,0.00006545795,0.00009637371],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0003642051,0.0002086928,0.01710546,0.0005719244,0.00009157321,0.8917111,0.000912647,0.000314576,0.004434029,0.006571883,0.006887419,0.07082652],"study_design_scores_gemma":[0.00008855962,0.0001120992,0.01239794,0.0003121484,0.00008600422,0.9557143,0.0003786689,0.0004964072,0.001813017,0.002611828,0.02594281,0.00004629428],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.6331879,0.1297367,0.01441668,0.03036141,0.005913013,0.0007880387,0.002287913,0.002565723,0.1807426],"genre_scores_gemma":[0.9315115,0.0256388,0.006020628,0.005847278,0.00477306,0.0001284845,0.0006220766,0.0001378759,0.02532027],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.007356626,"threshold_uncertainty_score":0.02461034,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02944812801192721,"score_gpt":0.3592068562262883,"score_spread":0.3297587282143611,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}