{"id":"W4400948152","doi":"10.1182/blood.2024025077","title":"Diagnostic guidelines for familial hemophagocytic lymphohistiocytosis revisited","year":2024,"lang":"en","type":"article","venue":"Blood","topic":"Autoimmune and Inflammatory Disorders Research","field":"Medicine","cited_by":80,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children; University of Toronto","funders":"National Institute of General Medical Sciences","keywords":"Hemophagocytic lymphohistiocytosis; Medicine; Macrophage activation syndrome; Immunology; Pediatrics; Expert opinion; Internal medicine; Arthritis; Disease; Intensive care medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002830846,0.0001475175,0.0003055393,0.000156531,0.00008707938,0.00005202121,0.00009924774,0.00009295947,0.0001837605],"category_scores_gemma":[0.003285474,0.0001210609,0.0001963321,0.0002808002,0.00005433499,0.00007563607,0.00004116215,0.0001065793,0.0002844139],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00005192979,"about_ca_system_score_gemma":0.0003839882,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00001881961,"about_ca_topic_score_gemma":9.842151e-7,"domain_scores_codex":[0.9987153,0.0000194708,0.0004078496,0.0002985734,0.0002636698,0.000295154],"domain_scores_gemma":[0.9988807,0.000382882,0.00002557785,0.0002906618,0.0003218751,0.00009834103],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0007917013,0.002123739,0.02031226,0.01442731,0.002457495,0.002333837,0.0008592847,0.00003270001,0.09209987,0.007378297,0.6163484,0.2408351],"study_design_scores_gemma":[0.01758481,0.001689867,0.01620203,0.003613824,0.002451402,0.0006274641,0.0003684946,0.01541641,0.04675879,0.001209888,0.8931886,0.000888395],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.8833827,0.09694743,0.002785481,0.006447937,0.0006112125,0.002541129,0.0001222804,0.0008015765,0.006360284],"genre_scores_gemma":[0.98317,0.002544695,0.002265916,0.001415818,0.001185493,0.0004102542,0.0001925476,0.00009558392,0.008719703],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.2768402,"threshold_uncertainty_score":0.4936721,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0518859045003072,"score_gpt":0.3574104626413462,"score_spread":0.305524558141039,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}