{"id":"W4402840630","doi":"10.1158/1078-0432.ccr-24-2100","title":"Update on Surveillance for Wilms Tumor and Hepatoblastoma in Beckwith–Wiedemann Syndrome and Other Predisposition Syndromes","year":2024,"lang":"en","type":"review","venue":"Clinical Cancer Research","topic":"Renal and related cancers","field":"Biochemistry, Genetics and Molecular Biology","cited_by":36,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children","funders":"National Cancer Institute; Deutsche Kinderkrebsstiftung; Hospital Research Foundation; Alex's Lemonade Stand Foundation for Childhood Cancer; St. Baldrick's Foundation; Rally Foundation; Damon Runyon Cancer Research Foundation","keywords":"Hepatoblastoma; Medicine; Wilms' tumor; Context (archaeology); Beckwith–Wiedemann syndrome; Genetic predisposition; Cancer; Pediatrics; Intensive care medicine; Pathology; Internal medicine; Disease; Genetics; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001450436,0.0005142378,0.001329,0.003100173,0.0002098535,0.00088679,0.00105785,0.001432878,0.0040322],"category_scores_gemma":[0.003717498,0.0002579786,0.001288028,0.002134406,0.0002516782,0.001137487,0.0006387332,0.001580632,0.001458665],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0007739493,"about_ca_system_score_gemma":0.00231337,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003182571,"about_ca_topic_score_gemma":0.006462525,"domain_scores_codex":[0.9994567,0.000149755,0.0001185906,0.00005204661,0.0001909343,0.00003190046],"domain_scores_gemma":[0.9981208,0.0009267886,0.0002430635,0.00003467732,0.0005905061,0.00008410117],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00007443775,0.00003702616,0.0003802635,0.02847528,0.0002471837,0.0002407927,0.00008688954,0.0002063789,0.0004611055,0.001967424,0.1231672,0.844656],"study_design_scores_gemma":[0.00003591571,0.00006893776,0.0013152,0.02133505,0.0006229148,0.001077993,0.00004592634,0.00006372211,0.0001246127,0.0008990985,0.974393,0.00001756692],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0001139296,0.995992,0.0001344137,0.001589675,0.0006974864,0.00001388584,0.0001311377,0.00001633716,0.001311253],"genre_scores_gemma":[0.0005602101,0.996503,0.0003263377,0.001412456,0.0004172311,0.00001659176,0.0002448923,0.000003329131,0.0005159184],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.0040322,"threshold_uncertainty_score":0.01348901,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.158365421307045,"score_gpt":0.5139456760334001,"score_spread":0.3555802547263552,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}