{"id":"W4405105000","doi":"10.1111/hae.15135","title":"International Society on Thrombosis and Haemostasis Clinical Practice Guideline for Treatment of Congenital Haemophilia—A Critical Appraisal","year":2024,"lang":"en","type":"article","venue":"Haemophilia","topic":"Hemophilia Treatment and Research","field":"Medicine","cited_by":8,"is_retracted":false,"has_abstract":true,"ca_institutions":"McMaster University; Queen's University; University of Toronto; SickKids Foundation; Hospital for Sick Children; Canadian Hemophilia Society","funders":"Chugai Pharmaceutical; Genentech; Grifols; Swedish Orphan Biovitrum; Siemens Healthineers; AstraZeneca; CSL Behring; HemoSonics; Regeneron Pharmaceuticals; Alnylam Pharmaceuticals; Novo Nordisk; Sanofi; Bayer; Pfizer; Amgen","keywords":"Medicine; Haemophilia; Critical appraisal; Observational study; Guideline; Evidence-based medicine; Randomized controlled trial; MEDLINE; Evidence-based practice; Scientific evidence; Intensive care medicine; Alternative medicine; Pediatrics; Surgery","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.05309563,0.002705918,0.005177239,0.017942,0.001962996,0.006673339,0.006173703,0.007142045,0.008350162],"category_scores_gemma":[0.2207689,0.001647658,0.007315482,0.01300106,0.003081301,0.003973749,0.003730292,0.009163568,0.005201683],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.01071704,"about_ca_system_score_gemma":0.06803803,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0169449,"about_ca_topic_score_gemma":0.01827469,"domain_scores_codex":[0.9238298,0.03096398,0.01715723,0.001814039,0.02495059,0.001284319],"domain_scores_gemma":[0.7709363,0.07298524,0.03255587,0.004150141,0.1150685,0.004303949],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001645552,0.00007025201,0.0008940873,0.1208684,0.0009995556,0.000370857,0.0009152559,0.0008252928,0.0003104655,0.004785905,0.6467224,0.223073],"study_design_scores_gemma":[0.0002854392,0.0001646958,0.002433703,0.503687,0.002409475,0.0005803832,0.000479137,0.0006160332,0.0003135965,0.007158883,0.4817545,0.0001171117],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"review","genre_gemma":"commentary","genre_scores_codex":[0.0009712224,0.7023891,0.01374572,0.2000335,0.03182609,0.01905097,0.006500501,0.0005853422,0.02489769],"genre_scores_gemma":[0.01136888,0.8346673,0.07102232,0.03078127,0.01014165,0.02409408,0.009708086,0.0002374998,0.007978966],"genre_candidate":"commentary","genre_consensus":null,"teacher_disagreement_score":0.05309563,"threshold_uncertainty_score":0.2807999,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.149779920179615,"score_gpt":0.5094672480652935,"score_spread":0.3596873278856785,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}