{"id":"W4405423266","doi":"10.1002/mus.28308","title":"Mortality Trends and Causes of Death in Myotonic Dystrophy Type 1 Patients From the UK Clinical Practice Research Datalink","year":2024,"lang":"en","type":"article","venue":"Muscle & Nerve","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":8,"is_retracted":false,"has_abstract":true,"ca_institutions":"Ottawa Hospital; Children's Hospital of Eastern Ontario; University of Ottawa","funders":"Canadian Institutes of Health Research; National Cancer Institute; Muscular Dystrophy Canada; National Institutes of Health; Canada Research Chairs; Division of Cancer Epidemiology and Genetics, National Cancer Institute; Canada Foundation for Innovation","keywords":"Medicine; Myotonic dystrophy; Hazard ratio; Internal medicine; Proportional hazards model; Population; Confidence interval; Cohort; Cause of death; Standardized mortality ratio; Cohort study; Surgery; Disease","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.002257107,0.0003109669,0.0008546142,0.004034969,0.0003445541,0.00110005,0.0006697815,0.0005483865,0.005774385],"category_scores_gemma":[0.02085752,0.0003971221,0.0005281714,0.008816479,0.0001950676,0.0005994824,0.001171221,0.0004923834,0.001502763],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001272409,"about_ca_system_score_gemma":0.001030344,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.02204573,"about_ca_topic_score_gemma":0.023286,"domain_scores_codex":[0.9937065,0.001734993,0.002032548,0.0009175056,0.00129275,0.0003156769],"domain_scores_gemma":[0.9681162,0.005782843,0.02029382,0.001397443,0.00329982,0.00110982],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0004350164,0.00002411993,0.9704216,0.001018284,0.0002136058,0.0001670875,0.0003036099,0.0001975878,0.0002434356,0.0001297639,0.01376617,0.0130799],"study_design_scores_gemma":[0.00006599452,0.00008118302,0.991792,0.0003299132,0.00007108365,0.0002495957,0.00007290272,0.0002242288,0.00007646903,0.00004605272,0.006977628,0.00001294301],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.6818144,0.01094716,0.001268939,0.001462386,0.0001134597,0.0005202076,0.2939057,0.0001678361,0.009799912],"genre_scores_gemma":[0.7748469,0.005085299,0.002126616,0.0007234364,0.0001390204,0.001192216,0.2126964,0.00004372977,0.003146493],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.02204573,"threshold_uncertainty_score":0.04383481,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.2136745862230243,"score_gpt":0.451735458768692,"score_spread":0.2380608725456677,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}