{"id":"W4406080293","doi":"10.1016/j.jdcr.2024.12.024","title":"Kaposi sarcoma posthematopoietic stem cell transplant for vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic syndrome","year":2025,"lang":"en","type":"article","venue":"JAAD Case Reports","topic":"Otitis Media and Relapsing Polychondritis","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":false,"ca_institutions":"BC Cancer Agency; Leukemia & Lymphoma Society of Canada; Vancouver General Hospital; University of British Columbia","funders":"","keywords":"Medicine; Sarcoma; Hematopoietic stem cell; Stem cell; Hematopoietic stem cell transplantation; Haematopoiesis; Immunology; Pathology; Oncology; Internal medicine; Transplantation; Genetics; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000298729,0.0006359715,0.0003757385,0.0009540534,0.000851405,0.0006196367,0.0004291958,0.001326366,0.002215208],"category_scores_gemma":[0.001044078,0.0002210177,0.000559815,0.0003917475,0.0006598073,0.0005932217,0.0003792276,0.001110281,0.0004313249],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005584938,"about_ca_system_score_gemma":0.0004372996,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000568474,"about_ca_topic_score_gemma":0.001103609,"domain_scores_codex":[0.9997742,0.00003127478,0.00002771743,0.0000399083,0.00005142686,0.00007558401],"domain_scores_gemma":[0.9994824,0.0002026628,0.00009750266,0.00005921792,0.00002498679,0.0001332632],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0001256243,0.00007149204,0.007927724,0.00003585279,0.00001874097,0.9842455,0.00009952007,0.000100999,0.003816983,0.0004735454,0.0001654591,0.002918515],"study_design_scores_gemma":[0.00004770619,0.0001633745,0.01755205,0.00001312372,0.00002420973,0.9788809,0.00006879704,0.0004386114,0.002071754,0.0002287134,0.0005034845,0.000007379201],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9854442,0.001060317,0.001631549,0.0007998351,0.0001214334,0.00009082657,0.0001542849,0.0001252412,0.01057223],"genre_scores_gemma":[0.9976827,0.0002382322,0.0004132551,0.0001727948,0.00009991031,0.00001155181,0.00006268514,0.000008382086,0.001310368],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002215208,"threshold_uncertainty_score":0.007410586,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.009284481192364444,"score_gpt":0.2499722033612787,"score_spread":0.2406877221689142,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}