{"id":"W4408161634","doi":"10.1002/mds.30158","title":"Spinocerebellar Ataxia Progression Measured with the Patient‐Reported Outcome Measure of Ataxia","year":2025,"lang":"en","type":"article","venue":"Movement Disorders","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":10,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre Hospitalier de l’Université de Montréal","funders":"MINDlink Foundation; National Institute of Neurological Disorders and Stroke; Once Upon A Time Foundation; National Ataxia Foundation","keywords":"Spinocerebellar ataxia; Ataxia; Medicine; Neurological disorder; Central nervous system disease; Clinical neurology; Measure (data warehouse); Physical medicine and rehabilitation; Psychology; Neuroscience; Internal medicine; Psychiatry; Computer science; Data mining","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001547784,0.0002769215,0.0002478989,0.0001079868,0.0002630532,0.00004524137,0.000424441,0.00004310837,0.00005202215],"category_scores_gemma":[0.0003521403,0.0001728945,0.0001111449,0.0006611033,0.0002810656,0.0000779133,0.0001571226,0.0001368332,0.000005727241],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00004048991,"about_ca_system_score_gemma":0.0001206437,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00003930356,"about_ca_topic_score_gemma":0.0001058254,"domain_scores_codex":[0.9974436,0.0002544556,0.0004460813,0.0005909288,0.0009233317,0.0003416693],"domain_scores_gemma":[0.9986658,0.0000758667,0.000312198,0.0007480396,0.0001270407,0.00007106833],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0003853421,0.0009412478,0.4343252,0.0001462889,0.0001076863,0.00001258278,0.0005040781,0.001129139,0.5381737,0.0009093963,0.009867314,0.01349805],"study_design_scores_gemma":[0.001285965,0.0003489054,0.073566,0.0001013906,0.0001145513,2.351234e-7,0.0004657022,0.000137704,0.9195847,0.001261399,0.002839148,0.0002943231],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9915333,0.0004531817,0.0007788521,0.00300437,0.0002073599,0.001417,0.00002781171,0.00007423419,0.002503933],"genre_scores_gemma":[0.9947156,0.00002699615,0.00006845833,0.004555838,0.000006829877,0.0001485612,0.00000573035,0.00002508193,0.0004469434],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.381411,"threshold_uncertainty_score":0.7050431,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02793657575451542,"score_gpt":0.2746309975029402,"score_spread":0.2466944217484248,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}