{"id":"W4408161746","doi":"10.1111/epi.18329","title":"Dravet syndrome: From neurodevelopmental to neurodegenerative disease?","year":2025,"lang":"en","type":"article","venue":"Epilepsia","topic":"Epilepsy research and treatment","field":"Medicine","cited_by":14,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Ottawa; BC Children's Hospital; University of Toronto; SickKids Foundation; University Health Network; University of British Columbia; Hospital for Sick Children; Kingston General Hospital; Ottawa Hospital; Toronto Western Hospital","funders":"Dravet Syndrome Foundation","keywords":"Dravet syndrome; Disease; Medicine; Neuroscience; Epilepsy; Psychiatry; Psychology; Pediatrics; Pathology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001820553,0.0005793798,0.0004513287,0.0006326347,0.000316842,0.0004275075,0.0002857184,0.0004326587,0.003150991],"category_scores_gemma":[0.001452817,0.00008881358,0.0001836774,0.000988152,0.0004651891,0.0006276177,0.0004523413,0.0004117209,0.0003575878],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002926021,"about_ca_system_score_gemma":0.0003455566,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001988966,"about_ca_topic_score_gemma":0.001826345,"domain_scores_codex":[0.9997422,0.00004574342,0.0000410431,0.00006821421,0.00005867699,0.00004419071],"domain_scores_gemma":[0.9996238,0.00006707924,0.0001876394,0.0000132865,0.00005060617,0.00005751315],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"theoretical_or_conceptual","study_design_scores_codex":[0.0004009509,0.00009635015,0.8568549,0.0002267666,0.00009973985,0.07421895,0.0005518635,0.0001656736,0.003572028,0.001412648,0.002242865,0.06015724],"study_design_scores_gemma":[0.00005837646,0.000304431,0.6209309,0.000523589,0.0001299678,0.3657461,0.001380357,0.0004913942,0.001281886,0.002268655,0.006845877,0.0000384478],"study_design_candidate":"theoretical_or_conceptual","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"review","genre_scores_codex":[0.9681787,0.02198592,0.0009740822,0.002262458,0.0001860198,0.00004265044,0.0007048712,0.00005005963,0.005615191],"genre_scores_gemma":[0.9901304,0.007489621,0.0004638054,0.0003361205,0.0001743917,0.00001883989,0.0003700067,0.000008084903,0.001008846],"genre_candidate":"review","genre_consensus":null,"teacher_disagreement_score":0.003150991,"threshold_uncertainty_score":0.01054114,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01403688392021841,"score_gpt":0.2997055486920301,"score_spread":0.2856686647718117,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}