{"id":"W4408240162","doi":"10.1016/j.jaip.2025.02.036","title":"Hereditary Angioedema With Normal C1 Inhibitor: A Quarter Century of Forward Progress and Persisting Obstacles","year":2025,"lang":"en","type":"review","venue":"The Journal of Allergy and Clinical Immunology In Practice","topic":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","field":"Medicine","cited_by":8,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"","keywords":"Medicine; Hereditary angioedema; Quarter (Canadian coin); Angioedema; C1-inhibitor; Dermatology; Pediatrics","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001278787,0.0007462067,0.002128249,0.002056482,0.0003259917,0.0014733,0.0008034601,0.001660285,0.003095845],"category_scores_gemma":[0.001861826,0.0002143945,0.0004898249,0.001925008,0.0007537389,0.002374895,0.0008467388,0.002769546,0.001084349],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000673704,"about_ca_system_score_gemma":0.001474109,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001033995,"about_ca_topic_score_gemma":0.002077742,"domain_scores_codex":[0.9995957,0.00008412125,0.00006743128,0.00005999452,0.0001623491,0.00003040308],"domain_scores_gemma":[0.9985246,0.0008918758,0.0001343641,0.00003057025,0.0003010602,0.0001175988],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.000130056,0.00005746031,0.0003458873,0.01390629,0.0001012485,0.0004322957,0.0000753283,0.0001687169,0.0006691668,0.003885665,0.07963958,0.9005883],"study_design_scores_gemma":[0.00005575957,0.00008149353,0.001102037,0.00795388,0.0001974734,0.002605843,0.0001450398,0.0001291738,0.0001458926,0.00313112,0.9844239,0.00002835843],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.00004167637,0.9986171,0.00004163906,0.0007210751,0.000361036,9.063654e-7,0.000005195062,0.000003872501,0.0002074105],"genre_scores_gemma":[0.0004101459,0.9976627,0.0001175599,0.0007490533,0.0008335365,0.000002021649,0.00001234849,0.000001288986,0.0002113464],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.003095845,"threshold_uncertainty_score":0.01035661,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02569263412719549,"score_gpt":0.3568912137001565,"score_spread":0.331198579572961,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}