{"id":"W4408537473","doi":"10.1007/s12311-025-01816-z","title":"A Tailored Home-Based Training Program Improved Ataxia Severity and Participation in Adults With ARSACS","year":2025,"lang":"en","type":"article","venue":"The Cerebellum","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre hospitalier de l'Université Laval; Centre for Interdisciplinary Research in Rehabilitation; Centre Intégré Universitaire de Santé et de Services Sociaux du Centre-Sud-de-l'Île-de-Montréal; Institut Universitaire de Gériatrie de Montréal; Centre Hospitalier Universitaire de Sherbrooke; Université du Québec à Montréal; Université de Sherbrooke; Cégep de Jonquière; Université Laval; Centre Intégré Universitaire de Santé et de Services Sociaux du Saguenay–Lac-Saint-Jean","funders":"Fonds de Recherche du Québec - Santé","keywords":"Medicine; Physical therapy; Ataxia; Balance (ability); Rehabilitation; Activities of daily living; Rating scale; Physical medicine and rehabilitation; Sitting; Test (biology); Berg Balance Scale; Psychology; Psychiatry","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001148442,0.0001492123,0.0001431375,0.00006831453,0.0001433468,0.00006683409,0.000175977,0.00003082842,0.000010397],"category_scores_gemma":[0.0002276375,0.0001044262,0.00002329598,0.0004538729,0.0002492962,0.00006709548,0.00005233553,0.0001272145,0.000002856199],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002183997,"about_ca_system_score_gemma":0.0001238399,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00005078636,"about_ca_topic_score_gemma":0.0003101869,"domain_scores_codex":[0.9987492,0.000237355,0.0001689959,0.0004080657,0.0001420291,0.0002943372],"domain_scores_gemma":[0.9993863,0.0001609694,0.00006617774,0.0002934379,0.00003162869,0.0000615123],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.004707377,0.00172686,0.05335861,0.0004469863,0.00003062281,0.00004289912,0.009344932,0.002667729,0.7565743,0.0009551085,0.0002010028,0.1699436],"study_design_scores_gemma":[0.003744794,0.0006363288,0.307323,0.0001750341,0.00005129051,0.00000252823,0.0004857269,0.08419722,0.602174,0.0006346583,0.0002417027,0.0003337178],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9976797,0.00003307774,0.0002055505,0.0007285654,0.00006298003,0.0009682147,0.00001201133,0.00008007247,0.0002297936],"genre_scores_gemma":[0.9985602,0.00000496672,0.0002443186,0.0007508814,0.00001358724,0.0002957046,0.000004156947,0.00001307565,0.0001130683],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.2539644,"threshold_uncertainty_score":0.4258376,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02195141952133318,"score_gpt":0.2763642153237003,"score_spread":0.2544127958023671,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}