{"id":"W4408537473","doi":"10.1007/s12311-025-01816-z","title":"A Tailored Home-Based Training Program Improved Ataxia Severity and Participation in Adults With ARSACS","year":2025,"lang":"en","type":"article","venue":"The Cerebellum","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre hospitalier de l'Université Laval; Centre for Interdisciplinary Research in Rehabilitation; Centre Intégré Universitaire de Santé et de Services Sociaux du Centre-Sud-de-l'Île-de-Montréal; Institut Universitaire de Gériatrie de Montréal; Centre Hospitalier Universitaire de Sherbrooke; Université du Québec à Montréal; Université de Sherbrooke; Cégep de Jonquière; Université Laval; Centre Intégré Universitaire de Santé et de Services Sociaux du Saguenay–Lac-Saint-Jean","funders":"Fonds de Recherche du Québec - Santé","keywords":"Medicine; Physical therapy; Ataxia; Balance (ability); Rehabilitation; Activities of daily living; Rating scale; Physical medicine and rehabilitation; Sitting; Test (biology); Berg Balance Scale; Psychology; Psychiatry","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000410275,0.0003447468,0.00056967,0.0002753518,0.0002760458,0.0001425135,0.000146506,0.0003225121,0.001215492],"category_scores_gemma":[0.0006748915,0.0001011087,0.0003898894,0.0001533091,0.0001003937,0.0001299091,0.0002396585,0.0002338148,0.00008128629],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001477435,"about_ca_system_score_gemma":0.0002462009,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001845803,"about_ca_topic_score_gemma":0.004244168,"domain_scores_codex":[0.9998137,0.00006462759,0.0000242128,0.00003457755,0.00002889831,0.00003405882],"domain_scores_gemma":[0.9998443,0.00003661422,0.00003006426,0.000007783477,0.00002557016,0.0000556114],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"observational","study_design_scores_codex":[0.05124953,0.1139295,0.1678076,0.002611764,0.001004443,0.0008683624,0.003769012,0.00211371,0.05963659,0.0001078085,0.001278337,0.5956234],"study_design_scores_gemma":[0.004224301,0.1562112,0.8333603,0.0001535439,0.0004130524,0.0001993746,0.000540216,0.001455235,0.002030691,0.00003991039,0.001343991,0.00002812184],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9995608,0.00008178812,0.0000585603,0.0000103169,0.000006012212,0.0000931477,0.0000155012,0.000006606241,0.0001672996],"genre_scores_gemma":[0.998814,0.0001259064,0.0004912799,0.00002865577,0.00001267364,0.0001430701,0.0000576079,0.000001379939,0.0003255391],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001845803,"threshold_uncertainty_score":0.004066229,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02195141952133318,"score_gpt":0.2763642153237003,"score_spread":0.2544127958023671,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}