{"id":"W4409785662","doi":"10.1182/blood.2024028035","title":"Clinical phenotype and pathophysiological mechanisms underlying qualitative low VWF","year":2025,"lang":"en","type":"article","venue":"Blood","topic":"Platelet Disorders and Treatments","field":"Medicine","cited_by":4,"is_retracted":false,"has_abstract":true,"ca_institutions":"Queen's University","funders":"National Institutes of Health; Amgen; ZonMw; LEO Pharma; Bristol-Myers Squibb; CSL Behring; Science Foundation Ireland; Swedish Orphan Biovitrum; Novo Nordisk; Daiichi Sankyo Europe; Sanofi; Alexion Pharmaceuticals; National Heart, Lung, and Blood Institute; Pfizer","keywords":"Phenotype; Pathophysiology; Medicine; Biology; Immunology; Genetics; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0007890023,0.0003671073,0.000311347,0.001786794,0.0002237837,0.0007502554,0.0004277532,0.0003387089,0.001799718],"category_scores_gemma":[0.002743684,0.0001401419,0.0002298641,0.0008539403,0.0007062757,0.0003332524,0.0004935447,0.0003811042,0.0004180091],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003352456,"about_ca_system_score_gemma":0.0002488465,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0008192831,"about_ca_topic_score_gemma":0.0003807501,"domain_scores_codex":[0.9995665,0.0001004771,0.00007103416,0.00009783827,0.00008573652,0.00007832826],"domain_scores_gemma":[0.9991356,0.0001754799,0.0004321601,0.00006150471,0.00009195008,0.0001033966],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002998395,0.0000333121,0.9715297,0.00005281056,0.00004735945,0.004491688,0.0001516264,0.0001359011,0.01170856,0.0003846077,0.0002658017,0.01089885],"study_design_scores_gemma":[0.00001948123,0.0001109803,0.9602234,0.0000393739,0.00003688138,0.03468512,0.0002386484,0.0007564942,0.002449417,0.0007781663,0.0006469829,0.00001497763],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9955019,0.0009268382,0.001453649,0.000184451,0.00001378242,0.00003580359,0.0002996497,0.00003299955,0.001550904],"genre_scores_gemma":[0.9992604,0.0001305521,0.0002661803,0.00003701355,0.00001613124,0.000006134751,0.0001879074,0.000005591441,0.0000901239],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001799718,"threshold_uncertainty_score":0.006020725,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.06043343708546355,"score_gpt":0.4016269543555995,"score_spread":0.3411935172701359,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}