{"id":"W4410442768","doi":"10.1016/j.revmed.2025.03.069","title":"Traitement par voie orale des crises d’angiœdème héréditaire (AEH) : résultats de l’étude de phase 3 KONFIDENT testant l’efficacité et la tolérance du sebetralstat pour le traitement des crises d’AEH dans la population européenne","year":2025,"lang":"fr","type":"article","venue":"La Revue de Médecine Interne","topic":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"Montfort Hospital","funders":"","keywords":"Medicine; Gynecology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.001602254,0.0008579203,0.001099014,0.0004133669,0.0003756196,0.000304431,0.0005204986,0.0003559502,0.0002224258],"category_scores_gemma":[0.001197584,0.0008910473,0.0005092379,0.0007644812,0.0005938763,0.0003656009,0.0001646366,0.0005585394,0.00001545605],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001090709,"about_ca_system_score_gemma":0.000669669,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00569463,"about_ca_topic_score_gemma":0.007157814,"domain_scores_codex":[0.9947387,0.001028529,0.001503103,0.0009418124,0.0004210499,0.001366787],"domain_scores_gemma":[0.9965914,0.001376058,0.000451174,0.0006083293,0.0003450841,0.0006279321],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001200901,0.00817004,0.6957875,0.003516702,0.001128262,0.002577827,0.02480982,0.007764496,0.04351652,0.02889228,0.006022388,0.1766133],"study_design_scores_gemma":[0.01147358,0.0008627119,0.9098749,0.008801434,0.001057777,0.001077509,0.004697377,0.01831299,0.02127569,0.008953273,0.01277629,0.0008365202],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.933483,0.01220973,0.03813148,0.01188341,0.0004960145,0.0009491155,0.0004556166,0.0002727117,0.002118896],"genre_scores_gemma":[0.981444,0.003146244,0.004902026,0.001156581,0.00074445,0.0001926162,0.0003057109,0.0001651234,0.00794322],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.2140874,"threshold_uncertainty_score":0.999354,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02336703491349052,"score_gpt":0.3196326297641776,"score_spread":0.2962655948506871,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}