{"id":"W4410509442","doi":"10.4081/dr.2025.10230","title":"Urbach-Wiethe syndrome: report of two clinical cases","year":2025,"lang":"en","type":"article","venue":"Dermatology Reports","topic":"Genital Health and Disease","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Surgical Specialties (Canada)","funders":"","keywords":"Medicine; Dysphagia; Genodermatosis; Dermatology; Mucocutaneous zone; Pediatrics; Acitretin; Crying; Rare disease; Disease; Surgery; Pathology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003791488,0.0001271586,0.0006572638,0.0001364211,0.00005369679,0.000002951158,0.00004449352,0.0001758986,0.00008552762],"category_scores_gemma":[0.001669847,0.0001084406,0.0002117715,0.0002177403,0.0002284221,0.00003241889,0.00005505445,0.0002152512,0.00001910851],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00001745511,"about_ca_system_score_gemma":0.0009690081,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00009950426,"about_ca_topic_score_gemma":0.00001222691,"domain_scores_codex":[0.9976418,0.00008856608,0.001476975,0.000359014,0.0001600219,0.00027365],"domain_scores_gemma":[0.9981043,0.0002278527,0.0004138569,0.0007710091,0.0001830938,0.0002998339],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"case_report","study_design_scores_codex":[0.00007530994,0.0002366587,0.6758289,0.0003214817,0.00003619211,0.3063298,0.000007951453,3.496798e-7,0.00001038867,0.0001514512,0.01653209,0.0004694654],"study_design_scores_gemma":[0.0007381809,0.00008696312,0.3704669,0.00005974687,0.0002594969,0.6155933,0.00003110414,0.00001385289,0.0003402423,0.00114622,0.01118958,0.00007438634],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9758866,0.001811859,0.00005467104,0.002595273,0.0009805271,0.0003795326,0.000003064411,0.00007430681,0.0182142],"genre_scores_gemma":[0.9948192,0.00001122243,0.0003916842,0.00207035,0.00002722512,0.00002624983,0.0000554612,0.000009864993,0.002588726],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.3092635,"threshold_uncertainty_score":0.4422079,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03325336966619889,"score_gpt":0.4201153039609173,"score_spread":0.3868619342947184,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}