{"id":"W4410509442","doi":"10.4081/dr.2025.10230","title":"Urbach-Wiethe syndrome: report of two clinical cases","year":2025,"lang":"en","type":"article","venue":"Dermatology Reports","topic":"Genital Health and Disease","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Surgical Specialties (Canada)","funders":"","keywords":"Medicine; Dysphagia; Genodermatosis; Dermatology; Mucocutaneous zone; Pediatrics; Acitretin; Crying; Rare disease; Disease; Surgery; Pathology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004355782,0.002891831,0.001201985,0.002154021,0.00186953,0.001636701,0.001392573,0.004289279,0.002472586],"category_scores_gemma":[0.003283673,0.001351686,0.0007880788,0.001553235,0.002442891,0.001393094,0.002195598,0.001657621,0.001218266],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0009302062,"about_ca_system_score_gemma":0.0006762092,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001832181,"about_ca_topic_score_gemma":0.001451483,"domain_scores_codex":[0.9989341,0.0001099243,0.0001313229,0.0003675195,0.0001169363,0.0003401636],"domain_scores_gemma":[0.9984331,0.000310637,0.0003288727,0.0001543071,0.0001047486,0.0006683842],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.00006488343,0.000113433,0.01412532,0.00004950266,0.00001927324,0.9804342,0.0004872771,0.00007976545,0.001457348,0.0001733179,0.0004980064,0.002497707],"study_design_scores_gemma":[0.00003021694,0.00008023353,0.00747314,0.00001100603,0.00001335106,0.9909533,0.0001687059,0.00008302836,0.0002700931,0.00009787275,0.0008031119,0.00001593419],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9823664,0.004978799,0.002841295,0.001089724,0.0003125007,0.0003595779,0.0002970801,0.0001689102,0.007585599],"genre_scores_gemma":[0.9948817,0.001458394,0.001156262,0.0004676153,0.0004708417,0.00009641048,0.0002081657,0.00002702166,0.001233547],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.004289279,"threshold_uncertainty_score":0.008271575,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03325336966619889,"score_gpt":0.4201153039609173,"score_spread":0.3868619342947184,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}